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Vestibular nerve dysfunction and decompression in Engelmann's disease

Published online by Cambridge University Press:  29 June 2007

William P. L. Hellier  and
Gerald B. Brookes
William P. L. Hellier
Affiliation:
Department of Neuro-otology, National Hospital for Neurology and Neurosurgery, Queen Square, London.
Gerald B. Brookes*
Affiliation:
Department of Neuro-otology, National Hospital for Neurology and Neurosurgery, Queen Square, London.
*
Address for correspondence: Mr. G. B. Brookes F.R.C.S., Consultant ENT and Neuro-otological Surgeon, National Hospital for Neurology and Neurosurgery, Queen Square, London WC1N 3BG.
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Abstract

Vestibular nerve dysfunction as the major neuro-otological symptom in one of the osteopetrosis group of bone disorders is unusual. We describe a patient with Engelmann's disease who presented in this manner and who benefited from an eighth nerve decompression procedure. Surgical decompression of the internal auditory meatus to relieve vertigo has to our knowledge not been previously reported in this condition.

Keywords

OsteopetrosisVestibular diseases
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 110 , Issue 5 , May 1996 , pp. 462 - 465
Copyright
Copyright © JLO (1984) Limited 1996

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References

Allen, D. T., Saunders, A. M., Northway, W. H., Williams, G. F., Schafer, I. A. (1970) Corticosteroids in the treatment of Engelmann's disease: progressive diaphyseal dysplasia. Paediatrics 46: 523–531.CrossRefGoogle ScholarPubMed
Benecke, J. E. (1993) Facial nerve dysfunction in osteopetrosis. Laryngoscope 103: 494–497.CrossRefGoogle ScholarPubMed
Brookes, G. B., Booth, J. B. (1987) Diseases of the temporal bone In Scott-Brown's Diseases of the Ear, Nose and Throat 4th Edition. Butterworth Scientific, London, pp 340–380.Google Scholar
Engelmann, G. (1929) Ein Fall von Osteopathia hyperostotica (sclerotisans) multiplex infantalis. Fortschritte auf dem Gebiete der Röntgenstrahlen und der Nuklearmedizin 1101–1106.Google Scholar
Hamersma, H. (1977) Facial nerve paralysis in the osteopetroses In Facial Nerve Surgery. Aesulapius Publishing Co. Birmingham, Ala. pp 555–572.Google Scholar
Hamersma, H., May, M. (1986) Osteopetrosis and facial palsy In The Facial Nerve. (May, M. ed.), Thieme Inc., New York, pp 469–476.Google Scholar
Johnston, C. C.Lavy, N., Lord, N., Vellios, F., Merritt, A. D., Diess, W. P. (1968) Osteopetrosis, Medicine 47: 149–167.CrossRefGoogle ScholarPubMed
Miyamoto, R. T., House, W. F., Brackmann, D. E. (1980) Neurotologic manifestations of the osteopetroses. Archives of Otolaryngology 106: 210–214.CrossRefGoogle ScholarPubMed
Sparkes, R. S., Graham, C. B. (1972) Camurati-Engelmann disease. Genetics and clinical manifestations with a review of the literature. Journal of Medical Genetics 9: 73–85.CrossRefGoogle ScholarPubMed