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Multiple symmetrical lipomatosis: case report and literature review

Published online by Cambridge University Press:  15 May 2012

K J Sia ,
I P Tang  and
T Y Tan
K J Sia*
Affiliation:
Department of Otorhinolaryngology, Faculty of Medicine, University of Malaya, Malaysia
I P Tang
Affiliation:
Department of Otorhinolaryngology, Faculty of Medicine, University of Malaya, Malaysia
T Y Tan
Affiliation:
Otorhinolaryngology Department, Sarawak General Hospital, Malaysia
*
Address for correspondence: Dr Kian Joo Sia, 14A, Lorong 4A, Jalan Pipit, 96000 Sibu, Sarawak, Malaysia Fax: 6 082419495 E-mail: kj_sia@yahoo.com
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Abstract

Objective:

To discuss the pathophysiology and various treatment methods of multiple symmetrical lipomatosis.

Case report:

We report a case of multiple symmetrical lipomatosis in a middle-aged man. He presented to us with an extensive, disfiguring neck mass. Clinical examination and computed tomography suggested a lipomatous mass without compression of vital neck structures. The proximity of the lipomatous mass to the carotid sheaths attracted our interest. We performed surgical excision in this case, because of the deep infiltrative behaviour of the lipoma. The benefits and drawbacks of liposuction and surgical excision of extensive neck lipomatosis are discussed.

Conclusion:

Surgical excision and liposuction are complementary treatments in the management of multiple symmetrical lipomatosis. Patients should be aware of the limitations of both surgical options, and the risk of lipoma recurrence, before surgery. The decision on the mode of surgery relies upon the disease extent, the patient's expectations and the surgeon's experience.

Keywords

Multiple Symmetrical LipomatosisMadelung DiseaseLipomaSurgical Procedure, Operative
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 126 , Issue 7 , July 2012 , pp. 756 - 758
Copyright
Copyright © JLO (1984) Limited 2012

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