Skip to main content Accessibility help

We use cookies to distinguish you from other users and to provide you with a better experience on our websites. Close this message to accept cookies or find out how to manage your cookie settings.

Close cookie message
×
  1. Home
  2. Search

Refine search

Refine search

Access:
Content type:
Publication date:
Apply   From and To filters
Subject: Show more
Journals Show more
Publishers: Show more
Societies Show more
Series: Show more
Collections: Show more

Actions for selected content:

Select all | Deselect all
  • View selected items
  • Export citations
  • Download PDF (zip)
  • Save to Kindle
  • Save to Dropbox
  • Save to Google Drive

Save Search

You can save your searches here and later view and run them again in "My saved searches".

Please provide a title, maximum of 40 characters.
Cancel
×

1 results

  • A rare case of Proteus syndrome

  • N D Zingade, N N Zingade
  • Journal:
    The Journal of Laryngology & Otology / Volume 122 / Issue 3 / March 2008
    Published online by Cambridge University Press:
    18 February 2008, e7
    Print publication:
    March 2008
  • Introduction:

    We report a rare case of Proteus syndrome which presented with dysphagia due to unilateral tonsillar hypertrophy.

    Case report:

    Our case had involvement of multiple organs in addition to bony deformities, namely, enlarged right parotid gland and right testis, verrucous naevus, varicose veins and abdominal lipoma. The features unique to this case were a larger right optic disc and expansion of the inner table of the skull.

    Discussion:

    A literature review revealed less than 100 bona fide, published cases which fit the revised diagnostic criteria proposed by Turner.

    Summary:

    The ENT manifestations of Proteus syndrome are high arched palate, gingival hypertrophy, malocclusion and overcrowding of teeth, hyperostosis of the external auditory meatus, and low nasal bridge. Our patient had a unilateral enlargement of the tonsil causing dysphagia, which was relieved by tonsillectomy.