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Cardiac resynchronisation therapy associated with pulmonary artery banding in an adult with severe right ventricular dysfunction after Mustard repair for complete transposition of the great arteries: results after 2 years of follow-up

Published online by Cambridge University Press:  12 February 2013

Luca Donazzan ,
Giovanni Stellin ,
Werner Guenther Rauhe ,
Lucio Bonazza ,
Josef Stuefer ,
Cristina Romeo  and
Roberto Crepaz
Luca Donazzan*
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
Giovanni Stellin
Affiliation:
Pediatric and Congenital Cardiac Surgical Unit, University of Padua, Padua, Italy
Werner Guenther Rauhe
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
Lucio Bonazza
Affiliation:
Department of Pneumology, San Maurizio Regional Hospital, Bolzano, Italy
Josef Stuefer
Affiliation:
Service of Radiology, San Maurizio Regional Hospital, Bolzano, Italy
Cristina Romeo
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
Roberto Crepaz
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
*
Correspondence to: Dr Luca Donazzan, MD, Department of Cardiology, San Maurizio Regional Hospital, Via L. Boehler 5, 39100 Bolzano, Italy. Tel: +390471909985; Fax: +390471909997; E-mail: luca.donazzan@asbz.it
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Abstract

Late dysfunction of the systemic right ventricle in patients with complete transposition of the great arteries after Mustard or Senning procedures and progressive deterioration of the clinical status has been demonstrated. However, evidence-based data on the effective therapy for systemic right ventricular dysfunction in these patients are yet to be defined. Our patient shows an improvement in the right ventricular systolic function, with a reduction in tricuspid regurgitation and a consequent better exercise tolerance after a hybrid approach consisting of an upgrading of a previous transvenous-implanted dual-chamber Implantable Cardiac Defibrillator to biventricular pacing associated with pulmonary artery banding via an anterior thoracotomy.

Keywords

Complete transposition of the great arteriescardiac resynchronisation therapycongestive cardiac failureechocardiography
Type
Original Articles
Information
Cardiology in the Young , Volume 24 , Issue 1 , February 2014 , pp. 99 - 104
Copyright
Copyright © Cambridge University Press 2013 

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