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Challenges in the primary prevention of sudden cardiac death in hypertrophic cardiomyopathy in the young

Part of: Advanced Imaging

Published online by Cambridge University Press:  06 July 2021

Hirokuni Yamazawa Open the ORCID record for Hirokuni Yamazawa [Opens in a new window] ,
Atsuhito Takeda Open the ORCID record for Atsuhito Takeda [Opens in a new window]  and
Gaku Izumi Open the ORCID record for Gaku Izumi [Opens in a new window]
Hirokuni Yamazawa*
Affiliation:
Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Hokkaido, Japan
Atsuhito Takeda
Affiliation:
Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Hokkaido, Japan
Gaku Izumi
Affiliation:
Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Hokkaido, Japan
*
Author for correspondence: Hirokuni Yamazawa, MD, PhD, Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, North 15 West 7, Kitaku Sapporo, Hokkaido 060-8638 Japan. Tel: 81 11 706 5954; Fax: 81 11 706 7898. E-mail: yamazawa@med.hokudai.ac.jp
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Abstract

A case of hypertrophic cardiomyopathy in the transition from childhood to adulthood, which was low risk by the conventional risk assessment model, medium risk by the adult risk prediction model, and high risk by the paediatric risk prediction model, was inserted an implantable cardioverter-defibrillator. Three years post-implantation, the patient was resuscitated with an appropriate discharge of cardioverter-defibrillator.

Keywords

Implantable cardioverter-defibrillatorhypertrophic cardiomyopathylate gadolinium enhancement-MRIprimary prevention of sudden cardiac deathrisk prediction model
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 1 , January 2022 , pp. 156 - 157
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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