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Descending aortic flow reversal in obstructed total anomalous pulmonary venous connection

Published online by Cambridge University Press:  08 April 2016

Anupama K. Nair*
Affiliation:
Department of Pediatric Cardiology, Fortis Escorts Heart Institute & Research Centre, Delhi, India
Sitaraman Radhakrishnan
Affiliation:
Department of Pediatric Cardiology, Fortis Escorts Heart Institute & Research Centre, Delhi, India
Krishna S. Iyer
Affiliation:
Department of Pediatric & Congenital Heart Surgery, Fortis Escorts Heart Institute & Research Centre, Delhi, India
*
Correspondence to: A. K. Nair, Department of Pediatric Cardiology, Fortis Escorts Heart Institute & Research Centre, 5th floor, Okhla Road, New Delhi, Delhi 110025, India. Tel: +91-9818811317; Fax: +91-11-26825013; E-mail: dranu80nair@gmail.com

Abstract

In this study, we present the case of a neonate with obstructed infracardiac total anomalous pulmonary venous connection with severe pulmonary hypertension and a patent ductus arteriosus with right-to-left shunting. The patient had an unusual finding of pandiastolic flow reversal in the upper descending thoracic aorta. He underwent emergency surgical re-routing of the pulmonary veins to the left atrium, and postoperative echocardiography showed disappearance of the descending aortic flow reversal. We hypothesise that in severely obstructed total anomalous pulmonary venous connection the left ventricular output may be extremely low, resulting in flow reversal in the descending aorta.

Type
Brief Reports
Copyright
© Cambridge University Press 2016 

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