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Double outlet right ventricle with unilateral absence of left pulmonary artery

Published online by Cambridge University Press:  20 September 2012

Murat Ugurlucan ,
Ahmet H. Arslan ,
Yahya Yildiz ,
Sibel Ay  and
Sertac Cicek
Murat Ugurlucan
Affiliation:
Anadolu Medical Center Hospital, Cardiovascular Surgery Clinic, Istanbul, Turkey
Ahmet H. Arslan
Affiliation:
Anadolu Medical Center Hospital, Cardiovascular Surgery Clinic, Istanbul, Turkey
Yahya Yildiz
Affiliation:
Anadolu Medical Center Hospital, Cardiovascular Surgery Clinic, Istanbul, Turkey
Sibel Ay
Affiliation:
Anadolu Medical Center Hospital, Cardiovascular Surgery Clinic, Istanbul, Turkey
Sertac Cicek*
Affiliation:
Anadolu Medical Center Hospital, Cardiovascular Surgery Clinic, Istanbul, Turkey
*
Correspondence to: Prof. Dr S. Cicek, MD, FACC, FACS, Anadolu Medical Center Hospital, Cardiovascular Surgery Clinic, Cumhuriyet Mahallesi, 2255 Sokak, No. 3, Gebze 41400, Kocaeli, Turkey. Tel: +90 262 678 50 67; Fax: +90 262 654 05 38; E-mail: sertac.cicek@anadolusaglik.org
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Abstract

Congenital absence of unilateral pulmonary artery, either as a primary defect or in combination with other congenital cardiovascular malformations, is very rare. Double outlet right ventricle pathology in combination with unilateral absence of pulmonary artery has only been reported once in the literature. In this report, we present our experience with double outlet right ventricle with unilateral absence of left pulmonary artery in a 3-year-old female patient who underwent a palliative procedure and was scheduled for correction.

Keywords

Double outlet right ventricletetralogy of Fallotventricular septal defectbranchsingle
Type
Brief Reports
Information
Cardiology in the Young , Volume 23 , Issue 3 , June 2013 , pp. 466 - 469
Copyright
Copyright © Cambridge University Press 2012 

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