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Late complications associated with the Fontan circulation

Published online by Cambridge University Press:  10 January 2006

Marshall L. Jacobs  and
Glenn Pelletier
Marshall L. Jacobs
Affiliation:
Section of Cardiothoracic Surgery, St. Christopher's Hospital for Children, Drexel University, Philadelphia, Pennsylvania, United States of America
Glenn Pelletier
Affiliation:
Section of Cardiothoracic Surgery, St. Christopher's Hospital for Children, Drexel University, Philadelphia, Pennsylvania, United States of America
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Extract

The recent significant reduction in operative mortality associated with surgical completion of the Fontan circulation is clearly multi-factorial. Better understanding of the fundamental physiological and anatomical issues have led to refinements in operative technique, early neutralization of potential risk factors, widespread use of a staged approach, and selective application of the concept of fenestration or incomplete partitioning. While further reduction of operative mortality is important, and may be anticipated in the future, major emphasis now must be placed on optimizing functional outcome, and understanding and managing the late complications associated with the unique physiology produced by the Fontan circulation.

Keywords

Double inlet ventricleprotein-losing enteropathyfunctionally univentricular circulationatrioventricular valvar atresia
Type
Research Article
Information
Cardiology in the Young , Volume 16 , Supplement S1: Controversies and Challenges in the Management of the Functionally Univentricular Heart , February 2006 , pp. 80 - 84
Copyright
© 2006 Cambridge University Press

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