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Myocardial ischaemia and valve insufficiency caused by a dysplastic aortic valve cusp: a previously unreported unique morphologic anomaly

Published online by Cambridge University Press:  11 June 2020

Sharmeen Samuel Open the ORCID record for Sharmeen Samuel [Opens in a new window] ,
Preeta Dhanantwari ,
Nilanjana Misra  and
David B. Meyer
Sharmeen Samuel*
Affiliation:
Section of Pediatric Cardiology, Departments of Pediatrics and Cardiovascular Surgery, Cohen’s Children’s Hospital, Northwell Health, Donald and Barbara Zucker School of Medicine at Hofstra University, New York, NY, USA
Preeta Dhanantwari
Affiliation:
Section of Pediatric Cardiology, Departments of Pediatrics and Cardiovascular Surgery, Cohen’s Children’s Hospital, Northwell Health, Donald and Barbara Zucker School of Medicine at Hofstra University, New York, NY, USA
Nilanjana Misra
Affiliation:
Section of Pediatric Cardiology, Departments of Pediatrics and Cardiovascular Surgery, Cohen’s Children’s Hospital, Northwell Health, Donald and Barbara Zucker School of Medicine at Hofstra University, New York, NY, USA
David B. Meyer
Affiliation:
Section of Pediatric Cardiology, Departments of Pediatrics and Cardiovascular Surgery, Cohen’s Children’s Hospital, Northwell Health, Donald and Barbara Zucker School of Medicine at Hofstra University, New York, NY, USA
*
Author for correspondence: Sharmeen Samuel, MD, 1111 Marcus Ave, 4B, New Hyde Park, NY11042, USA. Tel: +1 516 601 7200; Fax: +1 516 601 7380. E-mail: ssamuel21@northwell.edu
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Abstract

Isolated aortic regurgitation and myocardial infarction are a rare congenital defect among neonatal patients. We present a case of a neonate with an unusual aortic valve morphology causing both regurgitation and obstruction of the left coronary artery ostium. Despite both non-invasive and invasive imaging modalities, accurate diagnosis of the valve morphology was only determined by direct visualisation at the time of surgical repair. To the knowledge of authors, this particular aortic valve morphology in neonatal population has not been previously reported in the literature.

Keywords

Aortic regurgitationdysplastic aortic valve cuspmyocardial ischaemia
Type
Brief Report
Information
Cardiology in the Young , Volume 30 , Issue 7 , July 2020 , pp. 1046 - 1049
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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