Hostname: page-component-cd9895bd7-gxg78 Total loading time: 0 Render date: 2024-12-26T18:55:46.706Z Has data issue: false hasContentIssue false

Palliative vertical vein stenting in a critical neonate with obstructed infradiaphragmatic total anomalous pulmonary venous connection

Published online by Cambridge University Press:  02 February 2022

Kanupriya Chaturvedi
Affiliation:
Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Hospital for Child Heart Care, Naya Raipur, India
Apurva Deshmukh
Affiliation:
Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Hospital for Child Heart Care, Naya Raipur, India
Prashant Thakur
Affiliation:
Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Hospital for Child Heart Care, Naya Raipur, India
Amit Lal
Affiliation:
Department of Anesthesia, Fortis Hospital, Bengaluru, India
Atul Prabhu*
Affiliation:
Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Hospital for Child Heart Care, Naya Raipur, India
*
Author for correspondence: A. Prabhu, MD, FNB, Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Hospital for Child Heart Care, Naya Raipur, Chhattisgarh 492101, India. Tel: +91-7977129346; Fax: +91-7712970325. E-mail: dratul.prabhu@srisathyasaisanjeevani.com

Abstract

Neonatal total anomalous pulmonary venous connection has an incidence of about ∼1–2%.1 The clinical presentation of total anomalous pulmonary venous connection in the neonatal period is dependent on the presence or absence of pulmonary venous obstruction, which is usual when the veins connect to the umbilicovitelline system, as in infradiaphragmatic total anomalous pulmonary venous connection. Obstructed total anomalous pulmonary venous connection presents with severe respiratory distress, metabolic acidosis, and cyanosis and requires urgent surgical intervention. However, critically ill neonates with obstructed total anomalous pulmonary venous connection have a higher surgical morbidity and mortality, and pre-operative stabilisation can improve outcomes in them. We present a case of a septic term neonate with obstructed infradiaphragmatic total anomalous pulmonary venous connection who underwent emergency palliative stent placement for immediate relief of pulmonary venous obstruction.

Type
Brief Report
Copyright
© The Author(s), 2022. Published by Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Mehrizi, A, Hirsch, MS, Taussig, HB. Congenital heart disease in the neonatal period: autopsy study of 170 cases. J Pediatr 1964; 65: 721726.CrossRefGoogle ScholarPubMed
Husain, SA, Maldonado, E, Rasch, D, et al. Total anomalous pulmonary venous connection: factors associated with mortality and recurrent pulmonary venous obstruction. Ann Thorac Surg 2012; 94: 825831.CrossRefGoogle ScholarPubMed
Yong, MS, d’Udekem, Y, Robertson, T, et al. Outcomes of surgery for simple total anomalous pulmonary venous drainage in neonates. Ann Thorac Surg 2011; 91: 19211927.CrossRefGoogle ScholarPubMed
Al-Muhaya, MA, Najjar, AH, Jelly, AA, et al. Palliative emergency stenting of the vertical vein in obstructive supracardiac pulmonary venous drainage prior to surgical repair. J Saudi Heart Assoc 2019; 31: 6468.CrossRefGoogle ScholarPubMed
Bratincsák, A, Van Alstine, WG, Koren, L, et al. Elective stent implant in the obstructed vertical vein of supracardiac total anomalous pulmonary venous connection prior to operative repair. J Struct Heart Dis 2017; 3: 176179.CrossRefGoogle Scholar
Burroughs, JT, Edwards, JE. Total anomalous pulmonary venous connection. Am Heart J 1960; 59: 913931.CrossRefGoogle ScholarPubMed