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Pentalogy of Cantrell with double-outlet right ventricle: a case of surgical correction

Published online by Cambridge University Press:  21 December 2010

Yoshio Ootaki ,
James Strainic  and
Ross M. Ungerleider
Yoshio Ootaki*
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
James Strainic
Affiliation:
Division of Pediatric Cardiology, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
Ross M. Ungerleider
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
*
Correspondence to: Dr Y. Ootaki, Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, 11100 Euclid Avenue, Cleveland, Ohio 44106, United States of America. Tel: 216 844 3058; Fax: 216 844 3517; E-mail: y.ootaki@nifty.com
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Abstract

Pentalogy of Cantrell is characterised by a combination of severe defects in the middle of the chest including the sternum, diaphragm, heart, and abdominal wall. Mortality rate after cardiac surgery is usually high. We report a successful total correction of the cardiac defects in a case of Pentalogy of Cantrell with a double-outlet right ventricle prior to abdominal wall defect repair.

Keywords

Congenital cardiac defectcardiac surgeryomphalocele
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 2 , April 2011 , pp. 235 - 237
Copyright
Copyright © Cambridge University Press 2010

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References

1. Cantrell, JR, Haller, JA, Ravitch, MM. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium, and heart. Surg Gynecol Obstet 1958; 107: 602–614.Google ScholarPubMed
2. Vazquez-Jimenez, JF, Muehler, EG, Daebritz, S, et al. Cantrell's syndrome: a challenge to the surgeon. Ann Thorac Surg 1998; 65: 1178–1185.CrossRefGoogle ScholarPubMed
3. St Louis, JD. Pentalogy of Cantrell associated with hypoplastic left heart syndrome and herniation of the ventricular mass into the abdominal cavity. Interact Cardiovasc Thorac Surg 2006; 5: 200–201.CrossRefGoogle ScholarPubMed
4. van Hoorn, JH, Moonen, RM, Huysentruyt, CJ, van Heurn, LW, Offermans, JP, Mulder, AL. Pentalogy of Cantrell: two patients and a review to determine prognostic factors for optimal approach. Eur J Pediatr 2008; 167: 29–35.CrossRefGoogle Scholar
5. Takaya, J, Kitamura, N, Tsuji, K, et al. Pentalogy of Cantrell with a double-outlet right ventricle: 3.5-year follow-up in a prenatally diagnosed patient. Eur J Pediatr 2008; 167: 103–105.CrossRefGoogle Scholar
6. Korver, AM, Haas, F, Freund, MW, Strengers, JL. Pentalogy of Cantrell: successful early correction. Pediatr Cardiol 2008; 29: 146–149.CrossRefGoogle ScholarPubMed
7. Gao, Z, Duan, QJ, Zhang, ZW, Ying, LY, Ma, LL. Images in cardiovascular medicine: Pentalogy of Cantrell associated with thoracoabdominal ectopia cordis. Circulation 2009; 119: e483–e485.CrossRefGoogle ScholarPubMed
8. O'Gorman, CS, Tortoriello, TA, McMahon, CJ. Outcome of children with Pentalogy of Cantrell following cardiac surgery. Pediatr Cardiol 2009; 30: 426–430.CrossRefGoogle ScholarPubMed