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A rhabdomyoma in the right ventricle presenting as hemodynamics of hypoplastic right heart

Published online by Cambridge University Press:  05 August 2020

Daiji Takajo Open the ORCID record for Daiji Takajo [Opens in a new window]  and
Sanjeev Aggarwal
Daiji Takajo*
Affiliation:
Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Sanjeev Aggarwal
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
*
Author for correspondence: Daiji Takajo, Children’s Hospital of Michigan, 3901 Beaubien Boulevard, Detroit, MI48201, USA. Tel: +1 313 745 1892; Fax: +1 313 993 7118. E-mail: dt1449@gmail.com
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Abstract

Rhabdomyomas are the most common paediatric cardiac tumours. The natural history of these tumours is mostly benign, and the tumour usually regresses spontaneously. Although surgical resection of these tumours is one of the considerations in patients with ventricular outflow obstruction, a palliation with Blalock–Taussig shunt is an alternative approach with the hope of regression of the tumour over time. We report a case of prenatally diagnosed rhabdomyomas in the right ventricle and its outflow presenting as hemodynamic simulating hypoplastic right ventricle in a newborn. She required prostaglandin and Blalock–Taussig shunts palliation for pulmonary flow and subsequent regression of tumours.

Keywords

Rhabdomyomashypoplastic right ventricle physiologyBlalock–Taussig shunt
Type
Brief Report
Information
Cardiology in the Young , Volume 30 , Issue 10 , October 2020 , pp. 1527 - 1529
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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