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Sports participation in long QT syndrome

Published online by Cambridge University Press:  13 January 2017

Peter F. Aziz  and
Elizabeth V. Saarel
Peter F. Aziz*
Affiliation:
Department of Pediatric Cardiology, Cleveland Clinic Main Campus, Cleveland, Ohio, United States of America
Elizabeth V. Saarel
Affiliation:
Department of Pediatric Cardiology, Cleveland Clinic Main Campus, Cleveland, Ohio, United States of America
*
Correspondence to: P. F. Aziz MD, Department of Pediatric Cardiology, Cleveland Clinic Main Campus, Mail Code M41, 9500 Euclid Avenue, Cleveland, OH 44195, United States of America. Tel: +216 445 6532; Fax: +216 445 3692; E-mail: azizp@ccf.org
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Abstract

Untreated congenital long QT syndrome may result in potentially lethal ventricular tachycardia. In the most common type, risk of such an event has been linked to exercise. This originally resulted in very restrictive guidelines for sports participation in affected individuals. Although the complex interactions of a specific genotype, modifying cofactors, and risk are only now being explored, scientific evidence based on clinical experience now suggests that in many instances such restrictive guidelines are unwarranted. In particular, patients with this condition who are compliant with β-blocker therapy and who have never had symptoms during exertion are now enjoying the benefits of athletic activity.

Keywords

Long QT syndromesudden deathathletesports participation
Type
Original Articles
Information
Cardiology in the Young , Volume 27 , Supplement S1: Sudden Cardiac Arrest in the Young: A Contemporary Perspective , January 2017 , pp. S43 - S48
Copyright
© Cambridge University Press 2017 

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