Skip to main content Accessibility help

We use cookies to distinguish you from other users and to provide you with a better experience on our websites. Close this message to accept cookies or find out how to manage your cookie settings.

Close cookie message
×
  1. Home
  2. Search

Refine search

Refine search

Access:
Content type:
Publication date:
Apply   From and To filters
Subject: Show more
Journals Show more
Publishers: Show more
Societies Show more
Series: Show more
Collections: Show more

Actions for selected content:

Select all | Deselect all
  • View selected items
  • Export citations
  • Download PDF (zip)
  • Save to Kindle
  • Save to Dropbox
  • Save to Google Drive

Save Search

You can save your searches here and later view and run them again in "My saved searches".

Please provide a title, maximum of 40 characters.
Cancel
×

2 results

  • Chapter 11 - Pentalogy of Cantrell

  • from Section 2 - Right-Sided Obstructive Lesions
  • Edited by Laura K. Berenstain, James P. Spaeth
  • Book:
    Congenital Cardiac Anesthesia
    Published online:
    09 September 2021
    Print publication:
    16 September 2021, pp 64-69

  • Summary

    Pentalogy of Cantrell is a syndrome consisting of (1) a midline, supraumbilical abdominal wall defect; (2) a congenital heart defect; (3) a lower sternal defect; (4) an anterior diaphragmatic defect; and (5) a diaphragmatic pericardial defect. Patients present a challenge to both the surgeon and anesthesiologist in the operating room due to the wide spectrum of anomalies with various complexities they bring. Planning dictates a multidisciplinary approach involving neonatology, cardiology, cardiac surgery, general surgery, anesthesiology, and pertinent subspecialties to determine the best course of action. Generally, corrective strategies include separation of the peritoneal and pericardial cavities with coverage of midline defects, omphalocele correction, repair of intracardiac lesions, and restoration of the heart into the thoracic cavity, all while preserving/establishing musculoskeletal structural integrity and hemodynamic stability. The potential for significant cardiopulmonary compromise is high and must be understood and anticipated when caring for these patients.