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2 results

Ten-year-old boy with congenital long QT syndrome type 2 (LQTS2) and life-threatening electrical storm: a case report of successful treatment with mexiletine
Moa Wåström, Jean-Pierre Pfammatter
Journal:

Cardiology in the Young / Volume 32 / Issue 11 / November 2022

Published online by Cambridge University Press:

30 March 2022, pp. 1871-1872
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We present a case of a boy with long QT syndrome type 2, who was admitted after an out of hospital cardiac arrest due to ventricular fibrillation. Subsequently, all treatments – intravenous magnesium, optimisation of electrolytes, an isoproterenol infusion – failed to terminate his electrical storm. As a last option before left-sided cardiac sympathetic denervation, mexiletine was started and the electrical storm resolved completely.

Propranolol syrup to tablets change triggers electrical storm in Jervell-Lange-Nielsen syndrome
Javier Ramos-Jiménez, Inmaculada Sánchez-Perez, Nicolás Moreno-Mata, Javier Moreno-Planas
Journal:

Cardiology in the Young / Volume 31 / Issue 1 / January 2021

Published online by Cambridge University Press:

13 October 2020, pp. 141-143
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A 10-year-old girl with genetically confirmed Jervell-Lange-Nielsen syndrome treated with beta-blocker and developed electrical storm after changing propranolol syrup to tablets. Jervell-Lange-Nielsen is characterised by long QT and congenital sensorineural deafness, with high risk of malignant arrhythmias at early ages. Gastric involvement and achlorhydria may be present, with subsequent alteration of medication bioavailability which can trigger severe arrhythmic complications.

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2 results

Ten-year-old boy with congenital long QT syndrome type 2 (LQTS2) and life-threatening electrical storm: a case report of successful treatment with mexiletine

Propranolol syrup to tablets change triggers electrical storm in Jervell-Lange-Nielsen syndrome