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Fibrous Dysplasia of the Skull Base Presenting Acutely in an Adult

Published online by Cambridge University Press:  02 December 2014

F. Amoozegar  and
A. Guberman
F. Amoozegar*
Affiliation:
University of Ottawa, The Ottawa Hospital, Ottawa, ON, Canada
A. Guberman
Affiliation:
University of Ottawa, The Ottawa Hospital, Ottawa, ON, Canada
*
144 Costello Avenue, Ottawa, Ontario, K2H 7C5, Canada
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Fibrous dysplasia (FD) of the bone is an idiopathic disorder in which bone-forming mesenchyme develops abnormally. Here, we describe an unusual case in an adult, with recurrent acute headache and third nerve palsy due to FD of the skull base and low-grade fibrosarcoma.

A previously healthy 32-year-old female office clerk, presented with an eight day history of acute-onset, severe, right occipital and retro-orbital continuous headache, associated with nausea and vomiting. She had required dimenhydrinate, acetaminophen with 15 mg codeine, and meperidine with only mild relief of the headache. She also described a 5-day history of right eye ptosis which had progressed to eye closure by the time of presentation. She had otherwise been well, with no systemic or constitutional symptoms and no previous history of headaches.

Type
Peer Reviewed Letter
Information
Canadian Journal of Neurological Sciences , Volume 33 , Issue 3 , August 2006 , pp. 325 - 327
Copyright
Copyright © The Canadian Journal of Neurological 2006

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