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Parkinsonism with Neuroacanthocytosis

Published online by Cambridge University Press:  18 September 2015

R.F. Peppard ,
C.S. Lu ,
Nai-Shin Chu ,
P. Teal ,
W.R.W. Martin  and
D.B. Calne
R.F. Peppard
Affiliation:
Department of Medicine, University of British Columbia, Vancouver
C.S. Lu
Affiliation:
Department of Neurology, Chang Gung Memorial Hospital, Taipei, Taiwan, R.O.C.
Nai-Shin Chu
Affiliation:
Department of Neurology, Chang Gung Memorial Hospital, Taipei, Taiwan, R.O.C.
P. Teal
Affiliation:
Department of Medicine, University of British Columbia, Vancouver
W.R.W. Martin
Affiliation:
Department of Medicine, University of British Columbia, Vancouver
D.B. Calne*
Affiliation:
Department of Medicine, University of British Columbia, Vancouver
*
Division of Neurology, University Hospital, 2211 Wesbrook Mall, U.B.C., Vancouver, British Columbia, Canada V6T 1W5
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Abstract:

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Two patients with neuroacanthocytosis are described. One presented with parkinsonism and the other resembled diurnal dystonia of the Segawa type. Both patients responded well to dopaminomimetic therapy. A PET scan with fluorodopa revealed a nigrostriatal deficit in the first patient.

Résumé:

RÉSUMÉ:

Nous décrivons deux patients avec neuro-acanthocytose. Un des patients s'est présenté avec du parkinsonisme et l'autre avec une dystonie diurne de type Segawa. Les deux patients ont bien répondu à la thérapie dopaminomimétique. Un PET scan à la fluorodopa a révélé un déficit nigrostrié chez le premier patient.

Type
Original Articles
Information
Canadian Journal of Neurological Sciences , Volume 17 , Issue 3 , August 1990 , pp. 298 - 301
Copyright
Copyright © Canadian Neurological Sciences Federation 1990

References

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