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Spongiform Encephalopathy of Long Duration: A Family Study

Published online by Cambridge University Press:  18 September 2015

G.P.A. Rice ,
D.W. Paty ,
M.J. Ball ,
R. Tatham  and
A. Kertesz
G.P.A. Rice
Affiliation:
University Hospital and St. Joseph's Hospital, London University of Western Ontario, Homewood Sanitarium, Guelph, Ontario
D.W. Paty
Affiliation:
University Hospital and St. Joseph's Hospital, London University of Western Ontario, Homewood Sanitarium, Guelph, Ontario
M.J. Ball*
Affiliation:
University Hospital and St. Joseph's Hospital, London University of Western Ontario, Homewood Sanitarium, Guelph, Ontario
R. Tatham
Affiliation:
University Hospital and St. Joseph's Hospital, London University of Western Ontario, Homewood Sanitarium, Guelph, Ontario
A. Kertesz
Affiliation:
University Hospital and St. Joseph's Hospital, London University of Western Ontario, Homewood Sanitarium, Guelph, Ontario
*
University Hospital, 339 Windermere Road, London, Ontario, N6A 5A5, Canada
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Seven members of a family succumbed to prolonged dementing illnesses. In two, whose dementia lasted 10 years, spongiform encephalopathy was found at autopsy. This duration of illness has not been a feature in other instances of familial Creutzfeldt-Jakob disease.

Type
Research Article
Information
Canadian Journal of Neurological Sciences , Volume 7 , Issue 3 , August 1980 , pp. 171 - 176
Copyright
Copyright © Canadian Neurological Sciences Federation 1980

References

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