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Case of progressive facial hemiatrophy with cervical sympathetic hyperactivity as underlying aetiology

Published online by Cambridge University Press:  15 June 2012

H Monobe ,
K Miyano ,
R Kagoya  and
H Tojima
H Monobe*
Affiliation:
Department of Otolaryngology, Hitachi General Hospital, Ibaraki, Japan Department of Otolaryngology, NTT Medical Center Tokyo, Tokyo, Japan
K Miyano
Affiliation:
Department of Otolaryngology, Showa General Hospital, Tokyo, Japan
R Kagoya
Affiliation:
Department of Otolaryngology, Tokyo Metropolitan Tama Medical Center, Tokyo, Japan
H Tojima
Affiliation:
Department of Otolaryngology, Hitachi General Hospital, Ibaraki, Japan
*
Address for correspondence: Dr Hiroko Monobe, Department of Otolaryngology, NTT Medical Center Tokyo, 5-9-22, Higashigotanda, Shinagawa, Tokyo, 141-8625, Japan Fax: +81 3 3448 6582 E-mail: h-monobe@chime.ocn.ne.jp
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Abstract

Objective:

We report a case of progressive facial hemiatrophy with cervical sympathetic hyperactivity as a possible underlying aetiology, based on clinical findings, three-dimensional computed tomography and thermographic imaging.

Methods:

We present a case report in which we describe the investigation and clinical course of progressive facial hemiatrophy, and we also review the world literature on this condition.

Results:

To our knowledge, this is the first report in the world literature of progressive facial hemiatrophy with cervical sympathetic hyperactivity indicated as a possible underlying aetiology, based on clinical findings, three-dimensional computed tomography and thermographic imaging.

Conclusion:

This syndrome may lead to atrophy of the subcutaneous adipose tissue with hyperfunction of the vegetative system. Although this is a rare syndrome, otolaryngologists should be aware of its symptoms, aetiology and treatment.

Keywords

Progressive Facial HemiatrophyParry-Romberg DiseaseSympathetic Nervous SystemSympathectomyThermography
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 126 , Issue 7 , July 2012 , pp. 725 - 728
Copyright
Copyright © JLO (1984) Limited 2012

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