Hostname: page-component-cd9895bd7-p9bg8 Total loading time: 0 Render date: 2024-12-28T02:17:32.602Z Has data issue: false hasContentIssue false

Failure to control the airway in a patient with Hunter's syndrome

Published online by Cambridge University Press:  29 June 2007

Luis Gaitini
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Milo Fradis*
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Sonia Vaida
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Geoffrey Collins
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Millian Croitoru
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Mustafa Somri
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Zvi Borochovltz
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Avishai Golz
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
*
Address for correspondence: Milo Fradis, M.D., Department of Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, P.O.B. 4940, 31048 Haifa, Israel.

Abstract

Hunter's syndrome is due to recessively inherited mucopolysaccharide storage diseases. The anaesthetic complications in this syndrome are related to the organs involved in the disease, but pertain especially to upper airway obstruction problems. We report a patient with Hunter's syndrome who, while under general anaesthesia for a simple procedure (the introduction of bilateral grommets), suffered a fatal outcome.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1998

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

American Society of Anesthesiologists (1993) Practice guidelines for management of the difficult airway. A report by the American Society of Anesthesiologists Task Force on Management of the Difficult Airway. Anesthesiology 78: 597601.Google Scholar
Baines, D., Keneally, J. (1983) Anaesthetic implications of the mucopolysaccharidoses: a 15-year experience in a children's hospital. Anaesthesia and Intensive Care 11: 198:202.CrossRefGoogle Scholar
Bredenkamp, J. K., Smith, M. E., Dudley, J. P., Williams, J. C., Crumley, R. L., Crockett, D. M. (1992) Otolaryngologic manifestations of the mucopolysaccharidoses. Annals of Otology, Rhinology and Laryngology 101: 472478.CrossRefGoogle ScholarPubMed
Herrick, I. A., Rhine, E. J. (1988) The mucopolysaccharidoses and anaesthesia: a report of clinical experience. Canadian Journal of Anaesthesia 35: 6773.CrossRefGoogle ScholarPubMed
Kempthorne, P. M., Brown, T. C. K. (1983) Anaesthesia and the mucopolysaccharidoses: a survey of techniques and problems. Anaesthesia and Intensive Care 11: 203207.CrossRefGoogle ScholarPubMed
Moores, C., Rogers, J. G., McKenzie, I. M., Brown, T. C. (1996) Anaesthesia for children with mucopolysaccharidoses. Anaesthesia and Intensive Care 24: 459463.CrossRefGoogle ScholarPubMed
Semenza, G. L., Pyeritz, R. E. (1988) Respiratory complications of mucopolysaccharidestorage disorders. Medicine 67: 209219.CrossRefGoogle Scholar
Shapiro, J., Strome, M., Crocker, A. C. (1985) Airway obstruction and sleep apnea in Hurlers and Hunter's syndromes. Annals of Otology, Rhinology and Laryngology 94: 458461.CrossRefGoogle Scholar
Woolley, M. M., Morgan, S., Hays, D. M. (1967) Heritable disorders of connective tissue. Surgical and anesthetic problems. Journal of Pediatric Surgery 2: 325331.CrossRefGoogle ScholarPubMed
Young, I. D., Harper, P. S. (1982) Mild form of Hunter's syndrome: clinical delineation based on 31 cases. Archives of Disease in Childhood 57: 828836.CrossRefGoogle ScholarPubMed
Zlotogora, J., Schaap, T., Zeigler, M., Bach, G. (1991) Hunter's syndrome in Jews in Israel: further evidence for prenatal selection favouring the Hunter allele. Human Genetics 86: 531533.CrossRefGoogle ScholarPubMed