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Simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome

Published online by Cambridge University Press:  16 July 2015

A A Alsanosi
A A Alsanosi*
Affiliation:
Department of Otolaryngology, King Saud University, Riyadh, Kingdom of Saudi Arabia
*
Address for correspondence: Dr Abdulrahman Alsanosi, Department of Otolaryngology and Head and Neck Surgery, King Saud University, PO Box 245, Riyadh 11411, Kingdom of Saudi Arabia Fax: 00966 1 4775748 E-mail: sanosi@hotmail.com
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Abstract

Objective:

To report a rare case of simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome.

Method:

Case report.

Results:

A five-month-old boy with Usher syndrome and congenital profound bilateral deafness underwent simultaneous bilateral cochlear implantation. The decision to perform implantation in such a young child was based on his having a supportive family and the desire to foster his audiological development before his vision deteriorated. The subject experienced easily resolvable intra- and post-operative adverse events, and was first fitted with an externally worn audio processor four weeks after implantation. At 14 months of age, his audiological development was age-appropriate.

Conclusion:

Simultaneous bilateral cochlear implantation is possible, and even advisable, in children as young as five months old when performed by an experienced implantation team.

Keywords

HematomaBone MarrowUsher SyndromeHearing LossCochlear Implantation
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 129 , Issue 9 , September 2015 , pp. 919 - 922
Copyright
Copyright © JLO (1984) Limited 2015 

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References

1Strøm-Roum, H, Laurent, C, Wie, OB. Comparison of bilateral and unilateral cochlear implants in children with sequential surgery. Int J Pediatr Otorhinolaryngol 2011;76:95–9CrossRefGoogle ScholarPubMed
2Boons, T, Brokx, JP, Frijns, JH, Peeraer, L, Philips, B, Vermeulen, A et al. Effect of pediatric bilateral cochlear implantation on language development. Arch Pediatr Adolesc Med 2012;166:28–34CrossRefGoogle ScholarPubMed
3Asp, F, Mäki-Torkko, E, Karltorp, E, Harder, H, Hergils, L, Eskilsson, G et al. Bilateral versus unilateral cochlear implants in children: speech recognition, sound localization, and parental reports. Int J Audiol 2012;51:817–32CrossRefGoogle ScholarPubMed
4Vincent, C, Bébéar, JP, Radafy, E, Vaneecloo, FM, Ruzza, I, Lautissier, S et al. Bilateral cochlear implantation in children: localization and hearing in noise benefits. Int J Pediatr Otorhinolaryngol 2012;76:858–64CrossRefGoogle ScholarPubMed
5Strøm-Roum, H, Rødvik, AK, Osnes, TA, Fagerland, MW, Wie, OB. Sound localization ability in children with bilateral sequential cochlear implants. Int J Pediatr Otorhinolaryngol 2012;76:1245–8CrossRefGoogle ScholarPubMed
6Scherf, F, van Deun, L, van Wieringen, A, Wouters, J, Desloovere, C, Dhooge, I et al. Subjective benefits of sequential bilateral cochlear implantation in young children after 18 months of implant use. ORL J Otorhinolaryngol Relat Spec 2009;71:112–21CrossRefGoogle ScholarPubMed
7Scherf, FW, van Deun, L, van Wieringen, A, Wouters, J, Desloovere, C, Dhooge, I et al. Functional outcome of sequential bilateral cochlear implantation in young children: 36 months postoperative results. Int J Pediatr Otorhinolaryngol 2009;73:723–30CrossRefGoogle ScholarPubMed
8Sparreboom, M, Snik, AF, Mylanus, EA. Sequential bilateral cochlear implantation in children: quality of life. Arch Otolaryngol Head Neck Surg 2012;138:134–41CrossRefGoogle ScholarPubMed
9Gordon, KA, Papsin, BC. Benefits of short interimplant delays in children receiving bilateral cochlear implants. Otol Neurotol 2009;30:319–31CrossRefGoogle ScholarPubMed
10Grainger, J, Jonas, NE, Cochrane, LA. Simultaneous cochlear implantation in children: the Great Ormond Street experience. Cochlear Implants Int 2012;13:137–41CrossRefGoogle ScholarPubMed
11Broomfield, SJ, Murphy, J, Emmett, S, Wild, D, O'Donoghue, GM. Results of a prospective surgical audit of bilateral paediatric cochlear implantation in the UK. Cochlear Implants Int 2013;14:19–21CrossRefGoogle ScholarPubMed
12Ramsden, JD, Papsin, BC, Leung, R, James, A, Gordon, KA. Bilateral simultaneous cochlear implantation in children: our first 50 cases. Laryngoscope 2009;119:2444–8CrossRefGoogle ScholarPubMed
13Papsin, BC, Gordon, KA. Bilateral cochlear implants should be the standard for children with bilateral sensorineural deafness. Curr Opin Otolaryngol Head Neck Surg 2008;16:69–74CrossRefGoogle ScholarPubMed
14Maria, PL, Oghalai, JS. When is the best timing for the second implant in pediatric bilateral cochlear implantation? Laryngoscope 2014;124:1511–12CrossRefGoogle Scholar
15Ramsden, JD, Gordon, K, Aschendorff, A, Borucki, L, Bunne, M, Burdo, S et al. European Bilateral Pediatric Cochlear Implant Forum consensus statement. Otol Neurotol 2012;33:561–5CrossRefGoogle ScholarPubMed
16May-Mederake, B, Kuehn, H, Vogel, A, Keilmann, A, Bohnert, A, Mueller, S et al. Evaluation of auditory development in infants and toddlers who received cochlear implants under the age of 24 months with the LittlEARS Auditory Questionnaire. Int J Pediatr Otorhinolaryngol 2010;2010:1149–55CrossRefGoogle Scholar
17Archbold, S, Lutman, ME, Marshal, DH. Categories of auditory performance. Ann Otol Rhinol Laryngol Suppl 1995;166:312–14Google ScholarPubMed
18Keenan, RL, Shapiro, JH, Dawson, K. Frequency of anesthetic cardiac arrests in infants: effect of pediatric anesthesiologists. J Clin Anesth 1991;3:433–7CrossRefGoogle ScholarPubMed
19Morray, JP, Geiduschek, JM, Ramamoorthy, C, Haberkern, CM, Hackel, A, Caplan, RA et al. Anesthesia-related cardiac arrest in children: initial findings of the Pediatric Perioperative Cardiac Arrest (POCA) Registry. Anesthesiology 2000;93:6–14CrossRefGoogle ScholarPubMed
20Tiret, L, Nivoche, Y, Hatton, F, Desmonts, JM, Vourc'h, G. Complications related to anaesthesia in infants and children. A prospective survey of 40240 anaesthetics. Br J Anaesth 1988;61:263–9CrossRefGoogle ScholarPubMed
21Cosetti, M, Roland, JT Jr. Cochlear implantation in the very young child: issues unique to the under-1 population. Trends Amplif 2010;14:46–57CrossRefGoogle Scholar
22Peters, BR, Wyss, J, Manrique, M. Worldwide trends in bilateral cochlear implantation. Laryngoscope 2010;120:S17–44CrossRefGoogle ScholarPubMed
23Schramm, D. Canadian position statement on bilateral cochlear implantation. J Otolaryngol Head Neck Surg 2010;39:479–85Google ScholarPubMed
24Wie, OB. Language development in children after receiving bilateral cochlear implants between 5 and 18 months. Int J Pediatr Otorhinolaryngol 2010;74:1258–66CrossRefGoogle ScholarPubMed
25Chadha, NK, James, AL, Gordon, KA, Blaser, S, Papsin, BC. Bilateral cochlear implantation in children with anomalous cochleovestibular anatomy. Arch Otolaryngol Head Neck Surg 2009;135:903–9CrossRefGoogle ScholarPubMed
26Gordon, KA, Tanaka, S, Wong, DD, Stockley, T, Ramsden, JD, Jewell, S et al. Multiple effects of childhood deafness on cortical activity in children receiving bilateral cochlear implants simultaneously. Clin Neurophysiol 2011;122:823–33CrossRefGoogle ScholarPubMed
27Tait, M, Nikolopoulos, TP, De Raeve, L, Johnson, S, Datta, G, Karltorp, E et al. Bilateral versus unilateral cochlear implantation in young children. Int J Pediatr Otorhinolaryngol 2010;74:206–11CrossRefGoogle ScholarPubMed
28Migirov, L, Kronenberg, J. Bilateral, simultaneous cochlear implantation in children: surgical considerations. J Laryngol Otol 2009;123:837–9CrossRefGoogle ScholarPubMed