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An unusual cause of acute labyrinthine failure

Published online by Cambridge University Press:  29 June 2007

J. S. Mehta
Affiliation:
Department of Neurosurgery, King's College Hospital, London, UK.
M. M. Sharr*
Affiliation:
Department of Neurosurgery, King's College Hospital, London, UK.
*
Address for correspondence: Mr M. Sharr, Department of Neurosurgery, King's College Hospital, London 5E5 9RS. Fax: 0171 346 3820

Abstract

We report a case of a 40-year-old man presenting with acute vertigo and deafness. Computed tomography (CT) scanning at initial presentation was normal. However, one year later he developed numbness on the right side of his face and examination revealed fifth, seventh and eighth cranial nerve palsies as well as cerebellar dysfunction. Magnetic resonance imaging (MRI) demonstrated a cerebellopontine angle lesion. He underwent near total excision followed by neuro-axis irradiation. The main mass of the tumour projected into the cerebellopontine angle. Histology showed this to be a medulloblastoma. All features of this case are unusual; hence we discuss the pathogenesis and management of this very rare tumour.

Type
Oncology in Focus
Copyright
Copyright © JLO (1984) Limited 1998

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