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Auditory steady state response in auditory neuropathy

Published online by Cambridge University Press:  14 April 2010

A A Emara  and
T A Gabr
A A Emara*
Affiliation:
MD Audiology Unit, ENT Department, Tanta University, Cairo, Egypt
T A Gabr
Affiliation:
MD Audiology Unit, ENT Department, Tanta University, Cairo, Egypt
*
Address for correspondence: Dr Afaf Ahmed Emara, Assistant Professor of Audiology, Tanta University, 11 Hassan Radwan Street, Tanta, Egypt. E-mail: Afaf_emara@hotmail.com
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Abstract

Review:

Auditory neuropathy is a disorder characterised by preservation of outer hair cell function, with normal otoacoustic emissions and/or cochlear microphonics, but an absent or distorted auditory brainstem response.

Purpose:

This study aimed to objectively assess hearing thresholds in patients with auditory neuropathy, using the auditory steady state response.

Materials and methods:

Thirteen patients with auditory neuropathy and 15 normal hearing subjects were examined. Audiological evaluation included basic audiological tests, otoacoustic emissions, auditory brainstem response and auditory steady state response.

Results:

In the auditory neuropathy patients, the auditory brainstem response was absent in 11 patients, while the auditory steady state response was absent in only three.

Conclusion:

The auditory steady state response may serve as a valuable objective measure for assessing the hearing threshold across different frequencies in patients with auditory neuropathy. We recommend that auditory steady state response be used to complete the evaluation of patients with auditory neuropathy.

Keywords

Auditory NeuropathyCochleaAuditory Brainstem ResponseAudiometryOtoacoustic EmissionsPsychoacoustics
Type
Main Articles
Information
The Journal of Laryngology & Otology , Volume 124 , Issue 9 , September 2010 , pp. 950 - 956
Copyright
Copyright © JLO (1984) Limited 2010

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Footnotes

Presented at the 6th Tanta International Conference on Advanced Otorhinolaryngology, 15–16 January 2009, Scientific Sessions (Cairo Sheraton Hotel), Tanta, Egypt.

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