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Cochlear implantation in a case of Wegener's granulomatosis

Published online by Cambridge University Press:  29 June 2007

K. A. Abou-Elhmd
Affiliation:
Department of Otolaryngology, North Riding Infirmary, Middlesbrough, UK.
M. R. Hawthorne*
Affiliation:
Department of Otolaryngology, North Riding Infirmary, Middlesbrough, UK.
L. M. Flood
Affiliation:
Department of Otolaryngology, North Riding Infirmary, Middlesbrough, UK.
*
Address for correspondence: Mr M. Hawthorne, F.R.C.S., Consultant ENT Surgeon, North Riding Infirmary, Newport Road, Middlesbrough, Cleveland TS1 5JE. Fax: 01642-231154

Abstract

Cochlear implantation is now a routine clinical procedure for deaf patients in many countries (Gibson, 1987). It replaces the function of damaged cochlear hair cells and, therefore, detects sound and by electrical stimulation produces an appropriate signal in the remaining cochlear nerve fibres (House and Berliner, 1991). Wegener's granulomatosis is an uncommon auto-immune disease. It has a peak incidence at the fifth decade with slight male predominance. Nasal problems are the predominant presentation with otological manifestations presenting rarely. We report a case of Wegener's granulomatosis presenting with total hearing loss and after right cochlear implantation a free field threshold of 40 dB and 20 per cent Bamford-Kowal-Bench (BKB) speech test.

We conclude that Wegener's granulomatosis is not an absolute contraindication for cochlear implantation.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1996

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References

Bench, J., Bamford, J. (1979) Speech-hearing tests and the spoken language of hearing-impaired children. Academic Press, London.Google Scholar
Blatt, I. M., Lawrence, M. (1961) Otological manifestations of fatal granulomatosis of the respiratory tract. Archives of Otolaryngology 73: 639645.CrossRefGoogle Scholar
Bourdiniere, J., Jezequel, J., DeLabarthe, B., Ramee, M. P., Bourguet, J. (1973) Granulomatose De Wegener a forme otologique. Annals of Otolaryngology 90: 203212.Google Scholar
Fahey, J., Leonard, E., Churg, J., Godman, G. (1954) Wegener's granulomatosis. American Journal of Medicine 17: 169179.Google Scholar
Fauci, A. S., Haynes, B. F., Katz, P., Wolff, S. M. (1983) Wegener's granulomatosis: prospective clinical and therapeutic experience with 85 patients for over 21 years. American International Medicine 98: 7685.CrossRefGoogle Scholar
Friedmann, I., Bauer, F. (1973) Wegener's granulomatosis causing deafness. Journal of Laryngology and Otology 87: 445469.CrossRefGoogle ScholarPubMed
Gibson, W. P. (1987) Cochlear implants. In Scott-Brown's Otolaryngology. 5th Edition, (Booth, J. B., Kerr, A. G., Groves, J., eds.) Butterworth Co., London, pp 602617.Google Scholar
House, W. F., Berliner, K. (1991) Cochlear implants: from idea to clinical practice. In Cochlear Implants: A Practical Guide, (Cooper, H., ed.) Whurr, London, pp 933.Google Scholar
Ilium, P., Thorling, K. (1982) Otologic manifestations of Wegener's granulomatosis. Laryngoscope 92: 801804.Google Scholar
Ito, Y., Shinogo, J., Yuta, A., Okada, E., Taki, M., Matsukage, H. (1991) A case report of Wegener's granulomatosis limited to the ear. Auris Nasus Larynx 18: 281289.CrossRefGoogle ScholarPubMed
Karmody, C. S. (1978) Wegener's granulomatosis presentation as an otological problem. Otolaryngology-Head and Neck Surgery 86: 573584.CrossRefGoogle Scholar
Kornblut, A. D. (1982) Ear disease in patients with Wegener's granulomatosis. Laryngoscope 92: 713717.CrossRefGoogle ScholarPubMed
Linthicum, F. H., Schwartzman, I. (1972) Wegener's granulomatosis appearing initially as otitis media. Transactions of the American Academy of Ophthalmology and Otology 72: 304307.Google Scholar
McCaffrey, T. V., McDonald, T. J., Facer, G. W., DeRemee, R. A. (1980) Otologic manifestations of Wegener's granulomatosis. Otolaryngology – Head and Neck Surgery 88: 586593.CrossRefGoogle ScholarPubMed
McDonald, T. J., DeRemee, R. A. (1983) Wegener's granulomatosis. Laryngoscope 93: 220231.CrossRefGoogle ScholarPubMed
McDonald, T. J., DeRemee, R. A. (1993) Head and neck involvement in Wegener's granulomatosis. In ANCAAssociated Vasculitides: Immunological and Clinical Aspects. (Gross, W. L., ed.) Plenum Press, New York, pp. 309313.CrossRefGoogle Scholar
McDonald, T. J., DeRemee, R. A., Weiland, L. H. (1981) Wegener's granulomatosis and polymorphic reticulosis-two diseases or one? Experience with 90 patients. Archives of Otolaryngology 107: 141144.CrossRefGoogle ScholarPubMed
Murty, G. E. (1990) Wegener's granulomatosis: Otorhinolaryngological manifestations (review). Clinical Otolaryngology 15: 385393.CrossRefGoogle Scholar
Nicklasson, B., Stangeland, N. (1982) Wegener's granulomatosis presenting as otitis media. Journal of Laryngology and Otology 96: 277280.CrossRefGoogle ScholarPubMed
Novack, S. N., Pearson, C. M. (1971) Cyclophosphamide therapy in Wegener's granulomatosis. New England Journal of Medicine 284: 938942.CrossRefGoogle ScholarPubMed
Per-Lee, J. H., Parson, R. C. (1969) Vasculitis presenting as otitis media. Southern Medical Journal 62: 161165.CrossRefGoogle ScholarPubMed