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Endolymphatic sac tumour: case report and literature review

Published online by Cambridge University Press:  28 February 2013

J S Virk*
Affiliation:
Department of Otolaryngology and Head and Neck Surgery, Charing Cross Hospital, Imperial College Healthcare NHS Trust, London, UK
P S Randhawa
Affiliation:
Department of Otolaryngology and Head and Neck Surgery, University College London Hospitals NHS Trust, UK
S R Saeed
Affiliation:
Department of Otolaryngology and Head and Neck Surgery, University College London Hospitals NHS Trust, UK
*
Address for correspondence: Mr J S Virk, Department of Otolaryngology and Head and Neck Surgery, Charing Cross Hospital, Imperial College Healthcare, Fulham Palace Rd, London W6 8RF, UK Fax: + 44 (0)208 8693098 E-mail: j_v1rk@hotmail.com

Abstract

Objective:

To increase awareness of the presentation, diagnostic difficulties and management of endolymphatic sac tumours.

Case reports:

A 79-year-old man with a 6-month history of unilateral hearing loss, tinnitus and vertigo, who was suspected to have an endolymphatic sac tumour on imaging, underwent successful transmastoid-translabyrinthine resection. A 53-year-old man with unilateral hearing loss and pulsatile tinnitus underwent subtotal resection of a suspected paraganglioma, which was identified histologically. Due to interval growth, gamma knife radiosurgery was performed followed by subtotal petrosectomy, at which juncture an endolymphatic sac tumour was reported.

Methods:

A review of the world literature was carried out using Medline, which identified less than 150 reported cases of endolymphatic sac tumour.

Conclusion:

Endolymphatic sac tumours are rare lesions of the petrous temporal bone. Although benign, they can be locally destructive. At present, there is no consensus regarding the management and long-term follow up of these tumours. Surgical resection is usually favoured, although treatment with radiotherapy and gamma knife surgery has also been reported.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 2013

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Footnotes

Oral presentation, Semon Club, Guy's and St Thomas' Hospital, 15 May 2012, London, UK.

References

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