Hostname: page-component-cd9895bd7-q99xh Total loading time: 0 Render date: 2024-12-28T05:07:58.492Z Has data issue: false hasContentIssue false
  • English
  • Français

Large endolymphatic sac. A congenital deformity of the inner ear shown by magnetic resonance imaging

Published online by Cambridge University Press:  29 June 2007

P. D. Phelps ,
C. F. O. Mahoney  and
L. M. Luxon
P. D. Phelps*
Affiliation:
Department of Radiology, Royal National Throat, Nose and Ear HospitalLondon, UK.
C. F. O. Mahoney
Affiliation:
Department of Audiological Medicine. Great Ormond Street Hospital for ChildrenLondon, UK.
L. M. Luxon
Affiliation:
Institute of Laryngology and Otology, London, UK.
*
Address for correspondence: Dr P. D. Phelps, M.D., F.R.C.S., F.R.C.R., D.M.R.D., Consultant Radiologist, The Royal National Throat, Nose and Ear Hospital, Gray's Inn Road, London WC1X 8DA.
Get access Rights & Permissions [Opens in a new window]

Abstract

Fluctuant and progressive hearing impairment in a patient with a wide vestibular aqueduct has been called the ‘large vestibular aqueduct syndrome’. Recently reports of magnetic resonance imaging (MRI) studies describe enlargement of the endolymphatic sac and duct in patients shown to have large vestibular aqueducts by computed tomography (CT). A patient with progressive deafness was shown to have borderline or slightly enlarged vestibular aqueducts by re-formatted sagittal CT. However, MRI in axial and sagittal planes gave a more satisfactory demonstration of both aqueduct and endolymphatic sac enlargement.

Keywords

Magnetic resonance imagingTomography, X-ray computedVestibular aqueduct
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 111 , Issue 8 , August 1997 , pp. 754 - 756
Copyright
Copyright © JLO (1984) Limited 1997

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Chen, A., Francis, M., Ni, L., Cremers, C. W., Kimberling, W. J., Sato, Y., Phelps, P. D., Bellman, S. C., Wagner, M. J., Pembrey, M. (1995) Phenotypic manifestations of branchiooto-renal syndrome. American Journal of Medical Genetics 58(4): 365–370.Google Scholar
Emmett, J. R. (1985) The large vestibular aqueduct syndrome. American Journal of Otology 6: 387–403.Google Scholar
Harnsberger, H. R., Dahlen, R. T., Shelton, C., Gray, S. D., Parkin, J. L. (1995) Advanced techniques in magnetic resonance imaging in the evaluation of the large endolymphatic duct and sac syndrome. Laryngoscope 105: 1037–1042.Google Scholar
Hirsch, B. E., Weissman, J. L., Curtin, H. D., Kamerer, D. B. (1992) Magnetic resonance imaging of the large vestibular aqueduct. Archives of Otolaryngology – Head and Neck Surgery 118: 1124–1127.Google Scholar
Hvidberg-Hansen, J., Balslev-Jorgensen, M. (1986) The inner ear in Pendred's syndrome. Acta Otolaryngologica (Stockh) 102: 239–247.Google Scholar
Levenson, M. J., Parisier, S. C., Jacomb, M., Edelstein, D. R. (1989) The large vestibular aqueduct syndrome in children. Archives of Otolaryngology – Head and Neck Surgery 115: 54–58.CrossRefGoogle ScholarPubMed
Mondini, C. (1791) Anatomica surdi nati sectio, Bononiensis scientarium et artium instituto atque academia commentarii, Bononiae VII: 419–428.Google Scholar
Pendred, V. (1896) Deaf-mutism and goitre. Lancet II: 532.Google Scholar
Reussner, L. A., Dutcher, P. O., House, W. F. (1995) Large vestibular aqueduct syndrome with massive endolymphatic sacs. Otolaryngology – Head and Neck Surgery 113: 606–610.Google Scholar
Valvassori, G. E., Clemis, J. D. (1978) The large vestibular aqueduct syndrome. Laryngoscope 88: 723–728.Google Scholar