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Large vestibular aqueduct syndrome and stapes fixation

Published online by Cambridge University Press:  29 June 2007

A. Shirazi ,
J. E. Fenton  and
P. A. Fagan
A. Shirazi
Affiliation:
Department of Otology and Neuro-Otology, St Vincents Hospital, Darlinghurst, Sydney, Australia.
J. E. Fenton
Affiliation:
Department of Otology and Neuro-Otology, St Vincents Hospital, Darlinghurst, Sydney, Australia.
P. A. Fagan*
Affiliation:
Department of Otology and Neuro-Otology, St Vincents Hospital, Darlinghurst, Sydney, Australia.
*
Dr Paul Fagan, 352 Victoria Street, Darlinghurst, NSW 2010, Australia.
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Abstract

An abnormally large vestibular aqueduct has a well recognized association with inner ear anomalies and it has been assumed previously to be a variant of a Mondini type of deformity (Shuknecht, 1980; Emmett, 1985). The sole radiological finding in some patients with progressive sensorineural loss has been a large vestibular aqueduct (Valvassori and Clemis, 1978; Valvassori, 1983), which is now accepted as a separate clinical entity, i.e. the large vestibular aqueduct syndrome (LVAS).

A case is presented which is believed to be the first reported with unilateral LVAS and stapes fixation and also the first stapes gusher described in association with LVAS.

Keywords

Vestibular aqueductStapes surgeryHearing loss
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 108 , Issue 11 , November 1994 , pp. 989 - 990
Copyright
Copyright © JLO (1984) Limited 1994

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