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Neurofibroma of the supraglottic larynx in childhood

Published online by Cambridge University Press:  29 June 2007

Jenö Czigner  and
Gabriella Fekete-Szabó
Jenö Czigner*
Affiliation:
Clinic of Otolaryngology, Albert Szent-Györgyi Medical University, Szeged, Hungary.
Gabriella Fekete-Szabó
Affiliation:
Clinic of Otolaryngology, Albert Szent-Györgyi Medical University, Szeged, Hungary.
*
Jenö Czigner, M.D., A. Szent-Györgyi Medical University, Clinic of Otolaryngology, Tisza L. Krt. 111, H-6725 Szeged, Hungary.
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Abstract

The case of a male child with a benign neurogenic laryngeal tumour caused by von Recklinghausen's disease is presented. At the age of eight years, tracheostomy was necessary. The tumour, deforming the right half of the larynx and extending into the right half of the neck, was removed three years later. Following this procedure, decannulation was possible, and the patient has been free of laryngological complaints for six years.

Attention is drawn to the fact that autosomal dominantly inherited neurofibromatosis is a generalized benign tumour with a special form. If it involves any vital structure or forms a functional obstacle, meticulous surgical removal is necessary, and this provides good prospects over a long period.

Keywords

NeurofibromatosisLaryngeal neoplasmsSurgery
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 108 , Issue 2 , February 1994 , pp. 156 - 158
Copyright
Copyright © JLO (1984) Limited 1994

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