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Old age presentation of the Dandy-Walker syndrome associated with unilateral sudden sensorineural deafness and vertigo

Published online by Cambridge University Press:  08 March 2006

S. R. M. Freeman
Affiliation:
Department of Otorhinolaryngology, South Manchester University Hospitals Trust, Manchester, U.K.
P.H. Jones
Affiliation:
Department of Otorhinolaryngology, South Manchester University Hospitals Trust, Manchester, U.K.

Abstract

Adult presentation of the Dandy-Walker syndrome is extremely rare. We report a case where the patient was first diagnosed at 75 years of age because of sudden onset of unilateral senorineural deafness and episodic vertigo. He remained well for a further three years until developing the more classical adult presenting features of cognitive impairment, disordered gait and ataxia. The radiological and otological investigative findings are discussed, together with their implications.

Type
Research Article
Copyright
© Royal Society of Medicine Press Limited 2002

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