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Paget’s disease and cochlear implantation

Published online by Cambridge University Press:  08 March 2006

A. Bacciu
Affiliation:
Department of Otolaryngology, University of Parma, Italy
E. Pasanisi
Affiliation:
Department of Otolaryngology, University of Parma, Italy
V. Vincenti
Affiliation:
Department of Otolaryngology, University of Parma, Italy
F. Ingegnoli
Affiliation:
Department of Rheumatology, Gaetano Pini Institute, University of Milano, Italy
M. Guida
Affiliation:
Department of Otolaryngology, University of Parma, Italy
F. Panu
Affiliation:
Department of Otolaryngology, University of Parma, Italy
S. Bacciu
Affiliation:
Department of Otolaryngology, University of Parma, Italy

Abstract

Paget’s disease of bone is a common disorder of unresolved etiology characterized by excessive bone resorption followed by excessive bone formation. If the skull isaffected this may result in hearing loss and eventually develop into profound deafness. To date, no cases of cochlear implantation in patients with Paget’s disease have been reported.

The authors present a case of radiographically confirmed Paget’s disease of the skull in a 77-year-old man with a 20-year history of progressive bilateral sensorineural hearing losswho underwent cochlear implantation. A successful insertion of the Nucleus 24 Contour electrodearray was achieved without surgical and postoperative complications.

At the 10 months’ postoperative evaluation, the patient had gained useful open-set speech perception. In quiet conditions, his performance scores on the word and sentence recognition tests were 100 and 98 per cent, respectively. In the presence of noise (at +10 dB. signal-to-noise ratio), his performance scores on the word and sentence recognition tests were 96 and 94per cent, respectively.

Type
Research Article
Copyright
© 2004 Royal Society of Medicine Press

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