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Sudden sensorineural hearing loss in haemoglobin SC disease

Published online by Cambridge University Press:  29 June 2007

M. Ellis Tavin ,
John S. Rubin  and
Fernando J. Camacho
M. Ellis Tavin
Affiliation:
From the Department of Otorhinolaryngology, Albert Einstein College of Medicine, Bronx, NY, USA.
John S. Rubin*
Affiliation:
From the Department of Otorhinolaryngology, Albert Einstein College of Medicine, Bronx, NY, USA.
Fernando J. Camacho
Affiliation:
From the Department of Montefiore Medical Center, Bronx, NY, USA and the Department of Medicine, Section of Hematology, Albert Einstein College of Medicine, Bronx, NY, USA.
*
Dr John S. Rubin, M.D., F.A.C.S., 48 Sagamore Road, Bronxville, New York 10708, USA.
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Abstract

Presented herein is a case report of sudden sensorineural hearing loss in the setting of haemoglobin SC disease. The relationship of the two is rare; the authors have found that this is only the second report in the literature. In this instance, partial exchange transfusions were performed in an attempt to decrease viscosity and improve blood flow. Thereafter, hearing stabilized and then slowly improved. The evidence for the beneficial role of these transfusions in this setting is, at best, circumstantial, but it is theoretically sound and worthy of further study.

Keywords

Hearing loss, sensorineural, suddenHaemoglobin SC disease
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 107 , Issue 9 , September 1993 , pp. 831 - 833
Copyright
Copyright © JLO (1984) Limited 1993

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References

Anderson, R., Cassell, M., Mullinax, G. L., Chaplin, H. (1963) Effect of normal cells on viscosity of sickle-cell blood. Archives of Internal Medicine 111: 286–294.CrossRefGoogle ScholarPubMed
Babior, B. M., Stossel, T. P. (1984) Sickle cell anemia and related hemoglobinopathies. Hematology, a Pathophysiological Approach. Ch. 11, Churchill Livingstone, New York, pp 153–164.Google Scholar
Brody, J. I., Goldsmith, M. H., Park, S. K., Soltys, H. D. (1970) Symptomatic crises of sickle cell anemia treated by limited exchange transfusion. Annals of Internal Medicine 72: 327–330.CrossRefGoogle ScholarPubMed
Davey, R. J., Esposito, D. J., Jacobson, R. J., Corn, M. (1978) Partial exchange transfusion as treatment for hemoglobin SC disease in pregnancy. Archives of Internal Medicine 138: 937–939.CrossRefGoogle ScholarPubMed
Davis, E. C, Nilo, E. R. (1965) Hearing improvement induced by phlebotomy in polycythemia. Laryngoscope 75: 1847–1852.CrossRefGoogle ScholarPubMed
Hotaling, A. J., Hillstrom, R. P., Bazell, C. (1989) Sickle cell crisis and sensorineural hearing loss: case report and discussion. International Journal ofPediatric Otorhinolaryngology 17: 207–211.CrossRefGoogle Scholar
Khwarg, S. G., Feldman, S., Ligh, J., Straatsma, B. R. (1985) Exchange transfusion in sickling maculopathy. Retina 5: 227–229.CrossRefGoogle ScholarPubMed
Morgenstein, K. M., Manace, E. D. (1969) Temporal bone histopathology in sickle cell disease. Laryngoscope 79: 2172–2180.CrossRefGoogle ScholarPubMed
Morrison, A. W., Booth, J. B. (1970) Sudden deafness: an otological emergency. British Journal of Hospital Medicine 4: 287–298.Google Scholar
Orchik, D. J., Dunn, J. W. (1977) Sickle cell anemia and sudden deafness. Archives of Otolaryngology 103: 369–370.CrossRefGoogle ScholarPubMed
Serjeant, G. R., Ashcroft, M. T, Serjeant, B. E. (1973) The clinical features of haemoglobin SC disease in Jamaica. British Journal of Haematology 24: 491–501.CrossRefGoogle ScholarPubMed
Todd, G. B., Serjeant, G. R., Larson, M. R. (1973) Sensori-neural hearing loss in Jamaicans with SS disease. Acta Otolaryngologica 76: 268–272.CrossRefGoogle ScholarPubMed
Urban, G. E. (1973) Reversible sensori-neural hearing loss associated with sickle cell crisis. Laryngoscope 83: 633–638.CrossRefGoogle ScholarPubMed