Book contents
- Uncommon Causes of Stroke
- Uncommon Causes of Stroke
- Copyright page
- Contents
- List of Contributors
- Preface
- PART I: INFECTIOUS AND INFLAMMATORY CONDITIONS
- PART II: HEREDITARY AND GENETIC CONDITIONS AND MALFORMATIONS
- PART III: VASCULAR CONDITIONS OF THE EYES, EARS, AND BRAIN
- PART IV: DISORDERS INVOLVING ABNORMAL COAGULATION
- PART V: SYSTEMIC DISORDERS THAT ALSO INVOLVE THE CEREBROVASCULAR SYSTEM
- 43 MICROSCOPIC POLYANGIITIS AND POLYARTERITIS NODOSA
- 44 CHURG-STRAUSS SYNDROME
- 45 SYSTEMIC LUPUS ERYTHEMATOSUS
- 46 RHEUMATOID ARTHRITIS AND CEREBROVASCULAR DISEASE
- 47 HYPERVISCOSITY AND STROKE
- 48 CALCIUM, HYPERCALCEMIA, MAGNESIUM, AND BRAIN ISCHEMIA
- 49 STROKE AND SUBSTANCE ABUSE
- 50 CANCER AND PARANEOPLASTIC STROKES
- 51 KOHLMEIER-DEGOS’ DISEASE (MALIGNANT ATROPHIC PAPULOSIS)
- 52 STROKE IN PATIENTS WHO HAVE INFLAMMATORY BOWEL DISEASE
- 53 SWEET’S SYNDROME (ACUTE FEBRILE NEUTROPHILIC DERMATOSIS)
- 54 NEPHROTIC SYNDROME AND OTHER RENAL DISEASES AND STROKE
- 55 EPIDERMAL NEVUS SYNDROME
- 56 SNEDDON’S SYNDROME
- 57 MITOCHONDRIAL AND METABOLIC CAUSES OF STROKE
- 58 BONE DISORDERS AND CEREBROVASCULAR DISEASES
- 59 SCLERODERMA
- PART VI: NONINFLAMMATORY DISORDERS OF THE ARTERIAL WALL
- PART VII: VENOUS OCCLUSIVE CONDITIONS
- PART VIII: VASOSPASTIC CONDITIONS AND OTHER MISCELLANEOUS VASCULOPATHIES
- PART IX: OTHER MISCELLANEOUS CONDITIONS
- Index
55 - EPIDERMAL NEVUS SYNDROME
from PART V: - SYSTEMIC DISORDERS THAT ALSO INVOLVE THE CEREBROVASCULAR SYSTEM
Published online by Cambridge University Press: 06 January 2010
Book contents
- Uncommon Causes of Stroke
- Uncommon Causes of Stroke
- Copyright page
- Contents
- List of Contributors
- Preface
- PART I: INFECTIOUS AND INFLAMMATORY CONDITIONS
- PART II: HEREDITARY AND GENETIC CONDITIONS AND MALFORMATIONS
- PART III: VASCULAR CONDITIONS OF THE EYES, EARS, AND BRAIN
- PART IV: DISORDERS INVOLVING ABNORMAL COAGULATION
- PART V: SYSTEMIC DISORDERS THAT ALSO INVOLVE THE CEREBROVASCULAR SYSTEM
- 43 MICROSCOPIC POLYANGIITIS AND POLYARTERITIS NODOSA
- 44 CHURG-STRAUSS SYNDROME
- 45 SYSTEMIC LUPUS ERYTHEMATOSUS
- 46 RHEUMATOID ARTHRITIS AND CEREBROVASCULAR DISEASE
- 47 HYPERVISCOSITY AND STROKE
- 48 CALCIUM, HYPERCALCEMIA, MAGNESIUM, AND BRAIN ISCHEMIA
- 49 STROKE AND SUBSTANCE ABUSE
- 50 CANCER AND PARANEOPLASTIC STROKES
- 51 KOHLMEIER-DEGOS’ DISEASE (MALIGNANT ATROPHIC PAPULOSIS)
- 52 STROKE IN PATIENTS WHO HAVE INFLAMMATORY BOWEL DISEASE
- 53 SWEET’S SYNDROME (ACUTE FEBRILE NEUTROPHILIC DERMATOSIS)
- 54 NEPHROTIC SYNDROME AND OTHER RENAL DISEASES AND STROKE
- 55 EPIDERMAL NEVUS SYNDROME
- 56 SNEDDON’S SYNDROME
- 57 MITOCHONDRIAL AND METABOLIC CAUSES OF STROKE
- 58 BONE DISORDERS AND CEREBROVASCULAR DISEASES
- 59 SCLERODERMA
- PART VI: NONINFLAMMATORY DISORDERS OF THE ARTERIAL WALL
- PART VII: VENOUS OCCLUSIVE CONDITIONS
- PART VIII: VASOSPASTIC CONDITIONS AND OTHER MISCELLANEOUS VASCULOPATHIES
- PART IX: OTHER MISCELLANEOUS CONDITIONS
- Index
Summary
The epidermal nevus syndrome refers to the association of any epidermal nevus with extracutaneous abnormalities. The most common extracutaneous abnormalities are neurologic, skeletal, and ocular, although other organs may also be involved. Widespread use of magnetic resonance imaging (MRI) has resulted in an increasing appreciation of the role of cortical malformations in patients with neurological symptoms. Strokes and vascular abnormalities have been reported in patients with the epidermal nevus syndrome. Arteriovenous malformations and leptomeningeal angiomas have been found in some patients with the epidermal nevus syndrome. Generally, the diagnosis of an epidermal nevus is not in doubt. If there are any doubts, a skin biopsy should be obtained. Treatment of the nevus with dermabrasion, diathermy, laser treatment, and cryotherapy is associated with a fairly high risk of recurrence of the nevus. Focal resection of the epidermal nevus before puberty is advised because of the increased risk of tumor development.
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- Uncommon Causes of Stroke , pp. 401 - 404Publisher: Cambridge University PressPrint publication year: 2008