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Complete congenital obstruction of a scimitar vein in an infant with severe respiratory failure

Published online by Cambridge University Press:  12 August 2009

Alexandra Bauch
Affiliation:
Division of Cardiology, Department of Paediatrics, Hospital for Sick Children, University of Toronto, Toronto, Canada
Kyong-Jin Lee
Affiliation:
Division of Cardiology, Department of Paediatrics, Hospital for Sick Children, University of Toronto, Toronto, Canada
Shi-Joon Yoo*
Affiliation:
Division of Cardiology, Department of Paediatrics, Hospital for Sick Children, University of Toronto, Toronto, Canada Department of Diagnostic Imaging, Hospital for Sick Children, University of Toronto, Toronto, Canada
*
Correspondence to: Shi-Joon Yoo, MD, FRCPC, Professor of Medical Imaging and Paediatrics, University of Toronto, Section Head, Cardiac Imaging, Department of Diagnostic Imaging, Hospital for Sick Children, 555 University Avenue, Toronto, Ontario, Canada, M5GIX8. Tel: (416) 813-6037; Fax: (416) 813-7591; E-mail: shi-joon.yoo@sickkids.ca

Abstract

We report an infant of 3 1/2 months with complete obstruction of the venous component of the scimitar syndrome, a large atrial septal defect within the oval fossa, a common left pulmonary vein, and pulmonary hypertension. To the best of our knowledge, ours is the first description of complete congenital obstruction of a scimitar vein.

Type
Brief Report
Copyright
Copyright © Cambridge University Press 2009

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