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Large right ventricular sinusoids in an infant with aorta–left ventricular tunnel and proximal right coronary artery atresia

Part of: Cardiac Morphology

Published online by Cambridge University Press:  16 April 2018

Peter C. Chen ,
Joseph A. Spinner  and
Jeffrey S. Heinle
Peter C. Chen*
Affiliation:
Department of Congenital Heart Surgery, Texas Children’s Hospital, Baylor School of Medicine, Houston, TX 77030, USA
Joseph A. Spinner
Affiliation:
Department of Cardiology, Texas Children’s Hospital, Baylor School of Medicine, Houston, TX 77030, USA
Jeffrey S. Heinle
Affiliation:
Department of Congenital Heart Surgery, Texas Children’s Hospital, Baylor School of Medicine, Houston, TX 77030, USA
*
Author for correspondence: P. C. Chen, MD, Department of Congenital Heart Surgery, Texas Children’s Hospital, Baylor School of Medicine, Houston, TX 77030, USA. Tel: 919 423 7932; Fax: 713 798 8941; E-mail: peter.chen@bcm.edu
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Abstract

We report a 1-month-old infant diagnosed with an aorta–left ventricular tunnel, ventricular septal defect, and right coronary atresia with right ventricular sinusoids. The patient’s anatomy and physiology did not indicate right-ventricular-dependent coronary circulation, and therefore right ventricular decompression could be performed without compromising coronary perfusion during surgical correction. A detailed understanding of the coronary anatomy is critical in managing this defect when coronary anomalies are present.

Keywords

Aorta–left ventricular tunnelright-ventricular-dependent coronary circulationright ventricular sinusoidsright coronary artery atresia
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 7 , July 2018 , pp. 978 - 980
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Copyright
© Cambridge University Press 2018 

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