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Neonatal hypertrophic cardiomyopathy with duct-independent systemic blood flow

Published online by Cambridge University Press:  19 August 2008

Kenji Suda ,
Darlene P. Horton  and
Norman H. Silverman
Kenji Suda
Affiliation:
Department of Pediatrics and Cardiovascular Research Institute, University of California, San Francisco, USA
Darlene P. Horton
Affiliation:
Department of Pediatrics and Cardiovascular Research Institute, University of California, San Francisco, USA
Norman H. Silverman*
Affiliation:
Department of Pediatrics and Cardiovascular Research Institute, University of California, San Francisco, USA
*
Norman H. Silverman, MD. Pediatric Echocardiography Laboratory, University of California, San Francisco, 505 Parnassus Avenue, San Francisco, CA-94143-0214 Tel (415) 476-5887; Fax (415) 476-5875. email: norman_silverman@pedcard.gateway.ucsf.edu
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Abstract

We describe a newborn who had echocardiogaphic features of severe hypertrophic cardiomyopathy and duct-dependent systemic blood flow. Blood flow to the upper body could be maintained only by prostaglandin El, as in the case of hypoplastic left heart syndrome. Forward flow was gradually established from the left ventricle, and the patient weaned from prostaglandin El. Although the patient's mother had poorly controlled diabetes, the patient at 24 months of age shows residual but lessened ventricular hypertrophy and increased cavity size.

Keywords

Hypertrophic cardiomyopathyhypoplastic left ventriclematernal diabetespatent arterial ductprostaglandin El
Type
Brief-Reports
Information
Cardiology in the Young , Volume 7 , Issue 4 , October 1997 , pp. 446 - 449
Copyright
Copyright © Cambridge University Press 1997

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