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Percutaneous treatment of a double-drainage scimitar-like syndrome

Part of: Advanced Imaging

Published online by Cambridge University Press:  03 September 2021

Giovanni Meliota Open the ORCID record for Giovanni Meliota [Opens in a new window] ,
Pierluigi Zaza  and
Ugo Vairo
Giovanni Meliota*
Affiliation:
Pediatric Cardiology, Giovanni XXIII Pediatric Hospital, Bari, Italy
Pierluigi Zaza
Affiliation:
Pediatric Cardiology, Giovanni XXIII Pediatric Hospital, Bari, Italy
Ugo Vairo
Affiliation:
Pediatric Cardiology, Giovanni XXIII Pediatric Hospital, Bari, Italy
*
Author for correspondence: G. Meliota, MD, Pediatric Cardiology, Giovanni XXIII Pediatric Hospital, 207 Via Amendola, Bari70126, Italy. Tel: +39 080 5596698; Fax: +39 080 5596700. E-mail: giovanni.meliota@gmail.com
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Abstract

Scimitar syndrome is a rare variant of anomalous right pulmonary vein connection to the inferior vena cava and it is associated with other cardiopulmonary anomalies. It generally requires surgery and sometimes it may go unrecognised into adulthood. We report a unique case of a scimitar syndrome variant in a young adult, who was successfully treated percutaneously, after the first misdiagnosis of arrhythmogenic ventricular cardiomyopathy. The cardiac magnetic resonance unveiled the uncommon anatomical pattern, avoiding surgical repair. Cross-sectional imaging is extremely useful in the diagnosis and treatment planning of CHD in adults.

Keywords

Scimitar syndromepercutaneous treatmentcardiac magnetic resonance
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 5 , May 2022 , pp. 806 - 808
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

Schramel, FM, Westermann, CJ, Knaepen, PJ, van den Bosch, JM. The scimitar syndrome: clinical spectrum and surgical treatment. Eur Respir J 1995; 8: 196–201.CrossRefGoogle ScholarPubMed
Luciano, D, Laux, D, Boudjemline, Y, et al. Transcatheter therapy in partially abnormal pulmonary venous return with additional drainage to the left atrium. Int J Cardiol 2013; 170: 221–226.10.1016/j.ijcard.2013.10.061CrossRefGoogle Scholar
Lee, M-L, Yang, S-C, Yang, AD. Transcatheter occlusion of the isolated scimitar vein anomaly camouflaged under dual pulmonary venous drainage of the right lung by the amplatzer ductal occluder. Int J Cardiol 2007; 115: e90–e93.10.1016/j.ijcard.2006.08.093CrossRefGoogle Scholar
Forbess, LW, O’Laughlin, MP, Harrison, JK. Partially anomalous pulmonary venous connection: demonstration of dual drainage allowing nonsurgical correction. Cathet Cardiovasc Diagn 1998; 44: 330–335.3.0.CO;2-O>CrossRefGoogle ScholarPubMed