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Severe pulmonary hypertension secondary to a parachute-like mitral valve, with the left superior caval vein draining into the coronary sinus, in a girl with Turner's syndrome

Published online by Cambridge University Press:  24 May 2005

Marc van Heerde ,
Jaroslav Hruda  and
Mark G. Hazekamp
Marc van Heerde
Affiliation:
Department of Paediatrics, VU University Medical Center, Amsterdam, The Netherlands
Jaroslav Hruda
Affiliation:
Department of Paediatrics, VU University Medical Center, Amsterdam, The Netherlands
Mark G. Hazekamp
Affiliation:
Department of Cardiothoracic Surgery, Leiden University Medical Center, Leiden, The Netherlands
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Abstract

A 17-year-old girl with Turner's syndrome underwent two cardiac operations due to severe mitral stenosis with pulmonary hypertension, caused by a parachute-like mitral valve. The anomaly was associated with persistence of the left superior caval vein, which drained to the coronary sinus, and non-compaction of the left ventricular myocardium. The association of these lesions is rare in patients with Turner's syndrome.

Keywords

Mitral valveXO syndromeleft superior vena cava
Type
Brief Report
Information
Cardiology in the Young , Volume 13 , Issue 4 , August 2003 , pp. 364 - 366
Copyright
© 2003 Cambridge University Press

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