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A unique foetal case of left ventricular non-compaction associated with arrhythmia, structural cardiac anomalies, and agenesis of the ductus venosus

Published online by Cambridge University Press:  22 June 2015

Varsha Thakur ,
Edgar T. Jaeggi  and
Lynne E. Nield
Varsha Thakur
Affiliation:
Department of Paediatrics, Labatt Family Heart Centre, The Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada
Edgar T. Jaeggi
Affiliation:
Department of Paediatrics, Labatt Family Heart Centre, The Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada
Lynne E. Nield*
Affiliation:
Department of Paediatrics, Labatt Family Heart Centre, The Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada
*
Correspondence to: L. E. Nield, MD, FRCPC, Department of Paediatrics, Labatt Family Heart Centre, The Hospital for Sick Children, University of Toronto, 555 University Avenue, Toronto, Ontario, Canada, M5G 1X8. Tel: 416 813 6140; Fax: 416 813 7547; E-mail: lynne.nield@sickkids.ca
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Abstract

A 21-week gestational age foetus was diagnosed with left ventricular non-compaction, Ebstein’s anomaly, sinus bradycardia, first-degree heart block, and agenesis of the ductus venosus. The prognosis was guarded given the constellation of findings, and the foetus was monitored closely. Despite a potentially poor outcome, the foetus survived. Prognosis in foetally diagnosed left ventricular non-compaction is usually poor; however, rarely, foetuses can survive postnatally.

Keywords

Foetusnon-compactionechocardiographycardiomyopathy
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Supplement 2 , February 2016 , pp. 368 - 370
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Copyright
© Cambridge University Press 2015 

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References

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