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Cardiac anomalies associated with congenital absence of the portal vein

Published online by Cambridge University Press:  19 August 2008

Martial Massin ,
Alain Verloes  and
Paul Jamblin
Martial Massin*
Affiliation:
Division of Paediatric Cardiology, CHR Citadelle, University of Liège, Liège, Belgium
Alain Verloes
Affiliation:
Walloon University Centre for Human Genetics, CHR Citadelle, University of Liège, Liège, Belgium
Paul Jamblin
Affiliation:
Division of Paediatric Radiology, CHR Citadelle, University of Liège, Liège, Belgium
*
Dr Martial Massin, MD, Division of Paediatric Cardiology, CHR Citadelle (Univetsity of Liège), Boulevard du 12è de Ligne, 1, B-4000 Liège, Belgium. Tel: +32 42256111; Fax: +32 42264747; E-mail: Martiai.Massin @chrcitadelle.be
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Abstract

The authors discovered congenital absence of the portal vein, with visceral venous return to the right atrium, in a 5-year-old girl with aortic valvar stenosis. Interestingly, of the 19 patients, it was discovered that 11 reported with portal venous agenesis also had cardiac defects. We have, therefore, investigated the hypothesis that the congenital absence of the portal vein and the associated cardiac malformations may result from a similar embryologic insult, and that cardiac development may be affected by the systemic diversion of portal venous flow.

Keywords

Abnormalitieschildrenembryologyheart diseaseportal vein
Type
Brief Reports
Information
Cardiology in the Young , Volume 9 , Issue 5 , September 1999 , pp. 522 - 525
Copyright
Copyright © Cambridge University Press 1999

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