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A “congenitally corrected” variant of Ebstein’s anomaly

Part of: Cardiac Morphology

Published online by Cambridge University Press:  10 January 2018

Rengin Çetin Güvenç ,
Gökmen Akgün  and
Tolga S. Güvenç
Rengin Çetin Güvenç
Affiliation:
Department of Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
Gökmen Akgün
Affiliation:
Department of Pediatric Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
Tolga S. Güvenç*
Affiliation:
Department of Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
*
Correspondence to: T. S. Güvenç, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Tıbbiye Street No:13, Kadıköy, Istanbul, Turkey. Tel: +90 216 632 1818; Fax: +90 216 632 7124; E-mail: tsguvenc@gmail.com
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Abstract

Ebstein’s anomaly is a rare CHD that is characterised by caudal displacement of the functional tricuspid annulus and a dysfunctional tricuspid valve owing to a failure of proper leaflet coaptation. We present a balanced variant of Ebstein’s anomaly, in which the overgrowth of the septal leaflet had allowed proper coaptation of the tricuspid leaflets, thus preserving the valve function.

Keywords

Ebstein’s anomalytricuspid valveCHD
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 4 , April 2018 , pp. 608 - 610
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Copyright
© Cambridge University Press 2018 

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References

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Güvenç et al. supplementary material 1

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