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Congenitally palliated scimitar syndrome

Published online by Cambridge University Press:  24 October 2014

Massimiliano Cantinotti ,
Raffaele Giordano  and
Isabella Spadoni
Massimiliano Cantinotti
Affiliation:
Fondazione G. Monasterio CNR-Regione Toscana, Massa, Italy
Raffaele Giordano*
Affiliation:
Fondazione G. Monasterio CNR-Regione Toscana, Massa, Italy
Isabella Spadoni
Affiliation:
Fondazione G. Monasterio CNR-Regione Toscana, Massa, Italy
*
Correspondence to: R. Giordano, MD, Fondazione G. Monasterio CNR-Regione Toscana, Ospedale del Cuore, via Aurelia Sud, 54100 Massa, Italy. Tel: +39 3297099540; Fax: +39 0585493616; E-mail: raf_jordan@inwind.it
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Abstract

We present a rare case of scimitar syndrome in which the scimitar vessel, collecting all the right pulmonary veins, was stenotic at its junction, with the inferior caval vein and two anomalous vessels, connecting to the same venous collector, draining most of the flow to the left atrium.

We arbitrarily defined this rare anatomical variant as a congenitally palliated scimitar syndrome.

Keywords

Scimitar syndromeCHDpaediatric cardiac surgery
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Issue 6 , August 2015 , pp. 1218 - 1220
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Copyright
© Cambridge University Press 2014 

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