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Conversion of the modified Fontan operation to total cavopulmonary connection: a treatment for protein-losing enteropathy

Published online by Cambridge University Press:  19 August 2008

Gerd Stafanger ,
Gösta Pettersson  and
Joes Ramsøe Jacobsen
Gerd Stafanger*
Affiliation:
Department of Paediatrics and Cardiothoracic Surgery, Rigshospital, Copenhagen, Denmark
Gösta Pettersson
Affiliation:
Department of Paediatrics and Cardiothoracic Surgery, Rigshospital, Copenhagen, Denmark
Joes Ramsøe Jacobsen
Affiliation:
Department of Paediatrics and Cardiothoracic Surgery, Rigshospital, Copenhagen, Denmark
*
Gerd Stafanger, Department of Paediatrics GGK 5004, Rigshospital, Blegdamsvej 9, DK 2100 Copenhagen Ø, Denmark. Tel: 35453825, Fax: 42307386
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Abstract

We describe a patient with tricuspid atresia who, after a Fontan operation three years earlier, presented with severe protein-losing enteropathy. After conversion to a cavopulmonary connection, the symptoms regressed and substitution with albumin and immunoglobulin was no longer required.

Keywords

Tricuspid atresiaFontan operationprotein-losing enteropathy
Type
Brief Reports
Information
Cardiology in the Young , Volume 7 , Issue 3 , July 1997 , pp. 344 - 346
Copyright
Copyright © Cambridge University Press 1997

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References

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