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Double outlet right atrium with coexisting double inlet left ventricle and concordant ventriculoarterial connections: a fascinating variant of the Holmes heart

Published online by Cambridge University Press:  23 July 2010

Louise Coats*
Affiliation:
Department of Cardiology, Wansbeck Hospital, Northumberland, United Kingdom
Craig Runnett
Affiliation:
Department of Cardiology, Wansbeck Hospital, Northumberland, United Kingdom
Duwarakan K. Satchithananda
Affiliation:
Department of Cardiology, Wansbeck Hospital, Northumberland, United Kingdom
*
Correspondence to: Dr L. Coats, Department of Cardiology, Wansbeck Hospital, Woodhorn Lane, Ashington NE63 9JJ, Northumberland. Tel: 0844 811 8111; Fax: 0167 052 9414; E-mail: lecoats@doctors.org.uk

Abstract

Occasionally complex congenital cardiac disease presents for the first time in adulthood, encouraging us to reflect anew on our understanding of familiar conditions. A 59-year–old woman, who had had two normal pregnancies, attended with breathlessness and was found to have a double inlet left ventricle with concordant ventriculoarterial connections and a straddling tricuspid valve adherent to the malaligned ventricular septum.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 2010

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References

1. Holmes, AF. Case of malformation of the heart. Edinburgh Trans Medico-Chir Soc 1824; 1: 252254.Google ScholarPubMed
2. Abbott, ME. Unique case of malformation of the heart? Defect of the interventricular septum; rudimentary right ventricle; patent foramen ovale; great dilatation of right auricle and right auricular appendix. Montreal Med J 1901; 30: 522532.Google Scholar
3. Anderson, RH, Becker, AE, Freedom, RM, et al. Sequential segmental analysis of congenital heart disease. Pediatr Cardiol 1984; 5: 281287.CrossRefGoogle ScholarPubMed
4. Lambert, EC. Single ventricle with a rudimentary outlet chamber: case report. Bull Johns Hopkins Hosp 1951; 88: 231238.Google ScholarPubMed
5. Milo, S, Ho, SY, Macartney, FJ, et al. Straddling and overriding atrioventricular valves: morphology and classification. Am J Cardiol 1979; 44: 11221134.CrossRefGoogle Scholar
6. Isomatsu, Y, Kurosawa, H, Imai, Y. Straddling tricuspid valve without a ventricular septal defect. Br Heart J 1989; 62: 222224.CrossRefGoogle ScholarPubMed
7. Tham, EB, Wald, R, McElhinney, DB, et al. Outcome of fetuses and infants with double inlet single left ventricle. Am J Cardiol 2008; 101: 16521656.CrossRefGoogle ScholarPubMed
8. Hanley, FL. The one and a half ventricle repair – we can do it, but should we do it? J Thorac Cardiovasc Surg 1999; 117: 659661.CrossRefGoogle Scholar