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Double venous drainage in scimitar syndrome. Ideal anatomy for percutaneous complete cure

Published online by Cambridge University Press:  04 February 2011

Georgia Sarquella-Brugada ,
Fredy Prada  and
Carlos Mortera
Georgia Sarquella-Brugada*
Affiliation:
Department of Cardiology, Hospital Sant Joan de Déu, Barcelona, Spain
Fredy Prada
Affiliation:
Department of Cardiology, Hospital Sant Joan de Déu, Barcelona, Spain
Carlos Mortera
Affiliation:
Department of Cardiology, Hospital Sant Joan de Déu, Barcelona, Spain
*
Correspondence to: G. Sarquella-Brugada, MD, Department of Cardiology, Hospital Sant Joan de Déu, Avinguda de Sant Joan de Déu, 2, 08950 Esplugues de Llobregat, Spain. Tel: +34636578184; Fax: +34972590265; E-mail: georgia@brugada.org
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Abstract

Congenital venolobular or scimitar syndrome is a rare congenital cardiopulmonary anomaly consisting in a partial anomalous pulmonary venous drainage, lung hypoplasia, and anomalous systemic arterial supply to the lung. It can associate with other congenital disorders which will confer the clinical presentation and prognosis of these patients. In most of the cases, the therapeutic approach is partial, as anatomy allows only aberrant arterial embolisation. We present a 6-year-old girl with recurrent pulmonary infections, diagnosed as scimitar syndrome with double collector drainage to the inferior caval vein and left atrium, undergoing interventional catheterisation for complete correction of her disorder. The anomalous systemic artery supply was embolised and the anomalous venous drainage was occluded. The patient was asymptomatic during follow-up, which supports the interventional catheterisation approach as a valid therapeutic option in cases of scimitar syndrome with double venous drainage.

Keywords

Vascular anomalyinterventional treatment
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 3 , June 2011 , pp. 357 - 360
Copyright
Copyright © Cambridge University Press 2011

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