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Early presentation of endomyocardial fibrosis in a 22-month-old child: a case report

Published online by Cambridge University Press:  28 October 2010

Antoinette M. Cilliers ,
Paul E. Adams  and
Ana O. Mocumbi
Antoinette M. Cilliers*
Affiliation:
Division of Paediatric Cardiology, Department of Paediatrics, C.H. Baragwanath Hospital, University of the Witwatersrand, Johannesburg, South Africa
Paul E. Adams
Affiliation:
Division of Paediatric Cardiology, Department of Paediatrics, C.H. Baragwanath Hospital, University of the Witwatersrand, Johannesburg, South Africa
Ana O. Mocumbi
Affiliation:
Instituto do Coração, Mozambique
*
Correspondence to: Dr A. M. Cilliers, Division of Paediatric Cardiology, Department of Paediatrics, Chris Hani Baragwanath Hospital, Bertsham 2013, Johannesburg, South Africa. Tel: 27 11 933 1297; Fax: 27 11 938 9074; E-mail: amcilliers@icon.co.za
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Abstract

We present an unusual, biopsy-proven case of endomyocardial fibrosis in a 22-month-old male child, which progressed rapidly resulting in death. The patient was born to a father originating from Mozambique, where the disease is endemic but who had not himself travelled there, suggesting a genetic link. Other remarkable features were the presence of a right ventricular diverticulum, and a positive Mycoplasma pneumoniae immunoglobulin M enzyme-linked immunosorbent assay test.

Keywords

Myocardial fibrosisdiverticulummycoplasma pneumoniae
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 1 , February 2011 , pp. 101 - 103
Copyright
Copyright © Cambridge University Press 2010

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