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The electrocardiogram in Down syndrome

Published online by Cambridge University Press:  02 April 2014

Milagros Caro ,
Diego Conde ,
Andrés R. Pérez-Riera ,
Adail P. de Almeida  and
Adrian Baranchuk
Milagros Caro
Affiliation:
Department of Cardiology, Instituto Cardiovascular de Buenos Aires, Buenos Aires, Argentina
Diego Conde*
Affiliation:
Department of Cardiology, Instituto Cardiovascular de Buenos Aires, Buenos Aires, Argentina
Andrés R. Pérez-Riera
Affiliation:
Department of Cardiology, Electro-Vectorcardigraphic Section, ABC Medical School, ABC Foundation, Santo Andre, Sao Paulo, Brazil
Adail P. de Almeida
Affiliation:
Department of Cardiology, Universidade Federal do Ceará, Recife, Brazil
Adrian Baranchuk
Affiliation:
Department of Cardiology, Queen’s University, Kingston, Ontario, Canada
*
Correspondence: Dr D. Conde, MD, Blanco Encalada 1543, Buenos Aires 1428, Argentina. Tel: +54 9 11 381 6339; Fax: +54 11 4787 7500 ext 3170; E-mail: drconde@hotmail.com
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Abstract

Down syndrome is the most common chromosomal abnormality, with an incidence of one case in every 650 live births. It is strongly associated with heart disease, which constitutes the main cause of mortality during the first 2 years of life in this population. Most of the cardiac abnormalities in patients with Down syndrome can be suspected by analysing the surface 12-lead ECG. The purpose of this systematic review was to analyse all available published material on surface ECG and cardiac rhythm and conduction abnormalities in patients with Down syndrome to facilitate the search to the clinical cardiologist and paediatrician.

Keywords

Down syndrome21 trisomyelectrocardiographyelectrocardiogram
Type
Review Articles
Information
Cardiology in the Young , Volume 25 , Issue 1 , January 2015 , pp. 8 - 14
Copyright
© Cambridge University Press 2014 

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