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Functional near-tricuspid atresia in a patient with absent pulmonary valve and an intact ventricular septum

Published online by Cambridge University Press:  30 August 2016

Yasunobu Miki ,
Toshikatsu Tanaka  and
Yoshihiro Oshima
Yasunobu Miki*
Affiliation:
Department of Cardiology, Kobe Children’s Hospital, Hyogo, Japan
Toshikatsu Tanaka
Affiliation:
Department of Cardiology, Kobe Children’s Hospital, Hyogo, Japan
Yoshihiro Oshima
Affiliation:
Department of Cardiovascular Surgery, Kobe Children’s Hospital, Hyogo, Japan
*
Correspondence to: Y. Miki, Department of Cardiology, Kobe Children’s Hospital, 1-6-7 Minatojimamimamimachi, Chuo-ku, Kobe, Hyogo 650-0047, Japan. Tel: +81 078 945 7300; Fax: +81 078 302 1023; E-mail: mkysnb@gmail.com
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Abstract

Absent pulmonary valve with an intact ventricular septum is a rare malformation. We report a case of absent pulmonary valve and intact ventricular septum with functional near-tricuspid atresia caused by pulmonary regurgitation. Initial palliation with main pulmonary artery ligation and bilateral pulmonary artery banding was performed at 1 day of age. More antegrade flow across the tricuspid valve was recognised postoperatively, resulting in a successful right ventricular outflow tract reconstruction by a hand-sewn bileaflet polytetrafluoroethylene valve and modified Blalock–Taussig shunt at 11 days of age.

Keywords

Absent pulmonary valveintact ventricular septumfunctional near-tricuspid atresia
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 2 , March 2017 , pp. 391 - 393
Copyright
© Cambridge University Press 2016 

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