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Hypoplastic left heart syndrome with right aortic arch, bilateral arterial ducts and origin of the left subclavian artery from the left pulmonary artery

Published online by Cambridge University Press:  19 August 2008

Chandrakant R. Patel*
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Childrens Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Michael L. Specter
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Childrens Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Kenneth G. Zahka
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Childrens Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
*
Chandrakant R. Patel, MD, Rainbow Babies and Childrens Hospital, Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106, USA. Tel: (216) 844 3275; Fax: (216) 844 5478

Abstract

The rare association, in a left-sided heart with hypoplastic left heart syndrome, of right aortic arch, bilateral patent arterial ducts and origin of the left subclavian artery from the left pulmonary artery are described. Cardiac catheterization was performed because of the abnormal anatomy of the arch noted at echocardiographic examination. This abnormality is of surgical importance when planning the Norwood operation.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1999

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