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Isolated noncompaction of ventricular myocardium

Published online by Cambridge University Press:  15 August 2006

Huda Elshershari ,
Vedat Okutan  and
Alpay Çeliker
Huda Elshershari
Affiliation:
Department of Pediatric Cardiology, Ihsan Doǧramaci Children's Hospital, Hacettepe University, Ankara, Turkey
Vedat Okutan
Affiliation:
Department of Pediatric Cardiology, Ihsan Doǧramaci Children's Hospital, Hacettepe University, Ankara, Turkey
Alpay Çeliker
Affiliation:
Department of Pediatric Cardiology, Ihsan Doǧramaci Children's Hospital, Hacettepe University, Ankara, Turkey
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Abstract

Isolated noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy resulting from an arrest in normal endomyocardial embryogenesis. The diagnosis can be made echocardiographically, and the entity may be associated with problems of cardiac rhythm. We describe two illustrative cases, with Wolf-Parkinson-White syndrome in one, and left bundle branch block in the other. We emphasize that children with problems of rhythm and findings suggestive for left ventricular cardiomyopathy, either hypertrophic or dilated; should be investigated to exclude isolated noncompaction of the ventricular myocardium.

Keywords

Spongy myocardiumcongenital cardiomyopathyWolf-parkinson-White syndromeleft bundle branch block
Type
Brief Report
Information
Cardiology in the Young , Volume 11 , Issue 4 , July 2001 , pp. 472 - 475
Copyright
2001 Cambridge University Press

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