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Myocarditis, flail tricuspid valve, and normal rhythm: an exceptional form of neonatal cardiac lupus

Published online by Cambridge University Press:  02 May 2017

María-Teresa González-López ,
Ramón Pérez-Caballero-Martínez  and
Juan-Miguel Gil-Jaurena
María-Teresa González-López*
Affiliation:
Pediatric Cardiac Surgery Department, Gregorio Marañón Hospital, Madrid, Spain Gregorio Marañón Health Research Institute, Madrid, Spain
Ramón Pérez-Caballero-Martínez
Affiliation:
Pediatric Cardiac Surgery Department, Gregorio Marañón Hospital, Madrid, Spain Gregorio Marañón Health Research Institute, Madrid, Spain
Juan-Miguel Gil-Jaurena
Affiliation:
Pediatric Cardiac Surgery Department, Gregorio Marañón Hospital, Madrid, Spain Gregorio Marañón Health Research Institute, Madrid, Spain
*
Correspondence to: M.-T. González-López, MD, PhD, Pediatric Cardiac Surgery Department, Gregorio Marañón Hospital, C/ O’Donnell 48-50, 28009 Madrid, Spain. Tel: +34 616 23 19 44; Fax: +34 915 86 80 18; E-mail: draglezlopez@hotmail.com
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Abstract

Neonatal cardiac lupus is a rare, passively acquired autoimmune disease. We report a case of in utero myocarditis, confirmed postnatally, with papillary muscle rupture and severe tricuspid regurgitation after birth in the absence of conduction disturbances. Tricuspid repair was successfully performed with polytetrafluoroethylene neochordae. In this article, we discuss the pathophysiology, medical and surgical management, and implications at follow-up in this unique scenario.

Keywords

Lupusmyocarditisneonatetricuspidneochordae
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 7 , September 2017 , pp. 1419 - 1422
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Copyright
© Cambridge University Press 2017 

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References

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González-López supplementary material

González-López supplementary material

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